Acute Disseminated Encephalomyelitis: Current Perspectives.
acquired demyelination syndrome (ADS)
acute disseminated encephalomyelitis (ADEM)
multiple sclerosis (MS)
myelin oligodendrocyte glycoprotein antibody (MOG-Ab)
neuromyelitis optica spectrum disorder (NMOSD)
optic neuritis (ON)
Journal
Children (Basel, Switzerland)
ISSN: 2227-9067
Titre abrégé: Children (Basel)
Pays: Switzerland
ID NLM: 101648936
Informations de publication
Date de publication:
03 Nov 2020
03 Nov 2020
Historique:
received:
02
10
2020
revised:
26
10
2020
accepted:
29
10
2020
entrez:
6
11
2020
pubmed:
7
11
2020
medline:
7
11
2020
Statut:
epublish
Résumé
Acute disseminated encephalomyelitis (ADEM) is an immune-mediated central nervous system (CNS) disorder, characterized by polyfocal symptoms, encephalopathy and typical magnetic resonance imaging (MRI) findings, that especially affects young children. Advances in understanding CNS neuroimmune disorders as well as the association of myelin oligodendrocyte glycoprotein antibody (MOG-Ab) with both monophasic and recurrent forms of ADEM have led to new insights into its definition, management and outcome. In this review, we aim to provide an update based on current epidemiologic, clinical, radiological and immunopathological aspects and clinical outcome of ADEM.
Identifiants
pubmed: 33153097
pii: children7110210
doi: 10.3390/children7110210
pmc: PMC7692206
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
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