Fat Embolism Syndrome in Sickle Cell Disease.
Bone Marrow Necrosis
Exchange Transfusion
Fat Embolism Syndrome
Parvovirus B19
Sickle Cell Disease
Therapeutic Plasma Exchange
Journal
Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588
Informations de publication
Date de publication:
08 Nov 2020
08 Nov 2020
Historique:
received:
25
10
2020
revised:
05
11
2020
accepted:
07
11
2020
entrez:
11
11
2020
pubmed:
12
11
2020
medline:
12
11
2020
Statut:
epublish
Résumé
Fat embolism syndrome is a devastating complication of sickle cell disease resulting from extensive bone marrow necrosis and associated with high mortality rates, while survivors often suffer severe neurological sequelae. Despite that, the syndrome remains under-recognised and under-diagnosed. Paradoxically, it affects exclusively patients with mild forms of sickle cell disease, predominantly HbSC and HbSβ
Identifiants
pubmed: 33171683
pii: jcm9113601
doi: 10.3390/jcm9113601
pmc: PMC7695297
pii:
doi:
Types de publication
Journal Article
Langues
eng
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