Uterine PEComa initially misdiagnosed as a leiomyoma: Sonographic findings and review of the literature.
Doppler
leiomyoma
perivascular epithelioid cell tumor
ultrasound
uterus
Journal
Journal of clinical ultrasound : JCU
ISSN: 1097-0096
Titre abrégé: J Clin Ultrasound
Pays: United States
ID NLM: 0401663
Informations de publication
Date de publication:
Jun 2021
Jun 2021
Historique:
revised:
25
09
2020
received:
17
07
2020
accepted:
25
10
2020
pubmed:
17
11
2020
medline:
27
5
2021
entrez:
16
11
2020
Statut:
ppublish
Résumé
Perivascular epithelioid cell neoplasms (PEComas) are rare mesenchymal tumors with malignant potential that arise from gynecological organs in up to 25% of cases. The lack of data regarding the preoperative US features of uterine PEComas is reflected by the frequent misdiagnosis with leiomyomas. We describe the sonographic appearance of a richly vascularized cervical PEComa mimicking a myoma and report the analysis of six additional cases in the literature with a description of their ultrasound features. Most cases involved a single lesion arising from the uterine cervix with a rapid growth pattern, regular margins, heterogeneous echogenicity, absence of shadowing, and moderate-to-rich vascularity.
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
492-497Informations de copyright
© 2020 Wiley Periodicals LLC.
Références
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