M Mode Ultrasound and Tissue Doppler Imaging to Assess Diaphragm Feature in Late Onset Pompe Disease.

LOPD diaphragm ultrasound

Journal

Neurology international
ISSN: 2035-8385
Titre abrégé: Neurol Int
Pays: Switzerland
ID NLM: 101551564

Informations de publication

Date de publication:
13 Nov 2020
Historique:
received: 20 01 2020
accepted: 10 02 2020
entrez: 18 11 2020
pubmed: 19 11 2020
medline: 19 11 2020
Statut: epublish

Résumé

Late-onset Pompe disease (LOPD) is an autosomal recessive lysosomal storage disease. Clinical features include skeletal muscle deficiency and diaphragm weakness. Clinical management relies on supportive treatment and mechanical ventilation in patients with chronic respiratory failure. M mode ultrasound and sniff tissue Doppler imaging can be used to assess and follow diaphragm function.

Identifiants

pubmed: 33203058
pii: neurolint12030012
doi: 10.3390/neurolint12030012
pmc: PMC7768541
doi:

Types de publication

Case Reports

Langues

eng

Pagination

55-58

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Auteurs

Paris Meng (P)

Intensive Care Unit and Home Mechanical Ventilation Unit, Raymond Poincaré Hospital, APHP, 92380 Garches, France.

Adam Ogna (A)

Intensive Care Unit and Home Mechanical Ventilation Unit, Raymond Poincaré Hospital, APHP, 92380 Garches, France.

Abdallah Fayssoil (A)

Cardiology Unit, Paris Saclay University, Raymond Poincaré Hospital, APHP, 92380 Garches, France.

Classifications MeSH