Malignant triton tumor of the rectum - A case report and review of the literature.
Malignant peripheral nerve sheath tumors
Malignant triton tumor
Multimodal treatment
Rectal resection
Journal
International journal of surgery case reports
ISSN: 2210-2612
Titre abrégé: Int J Surg Case Rep
Pays: Netherlands
ID NLM: 101529872
Informations de publication
Date de publication:
2020
2020
Historique:
received:
27
08
2020
revised:
06
10
2020
accepted:
07
10
2020
entrez:
19
11
2020
pubmed:
20
11
2020
medline:
20
11
2020
Statut:
ppublish
Résumé
Malignant triton tumors (MTT) are rare but highly aggressive tumors that originate from the Schwann cells. These tumors can occur in any part of the body, mostly present late and carry poor prognosis. We present a 24-year-old man with a rectal MTT causing non-specific abdominal pain and recurring ileus. The MRI showed a rectal mass near the urinary bladder with compression on the seminal vesical. A complete surgical resection of the tumor was performed. The immunohistological report confirmed a rectal MTT. Because of persistent ileus during the post-operative palliative chemotherapy, another tumor debulking was performed. The patient died 9 months after the diagnosis of MTT due to local recurrence under chemotherapy. MTTs are uncommon tumors in young age with high morbidity and mortality because of local recurrence also after complete resection.
Identifiants
pubmed: 33207422
pii: S2210-2612(20)30905-6
doi: 10.1016/j.ijscr.2020.10.027
pmc: PMC7596012
pii:
doi:
Types de publication
Case Reports
Langues
eng
Pagination
517-521Informations de copyright
Copyright © 2020 The Authors. Published by Elsevier Ltd.. All rights reserved.