Pulmonary Manifestations of Systemic Vasculitis in Children.


Journal

Pediatric clinics of North America
ISSN: 1557-8240
Titre abrégé: Pediatr Clin North Am
Pays: United States
ID NLM: 0401126

Informations de publication

Date de publication:
02 2021
Historique:
entrez: 24 11 2020
pubmed: 25 11 2020
medline: 27 4 2021
Statut: ppublish

Résumé

Vasculitides are defined according to the vessel size involved, and they tend to affect certain organ systems. Pulmonary involvement is rare in the common childhood vasculitides, such as Kawasaki disease, IgA vasculitis (Henoch Schonlein purpura). On the other hand, lung involvement is common in a rare pediatric vasculitis, granulomatosis with polyangiitis (GPA) (Wegener granulomatosis), where respiratory system findings are common. A criterion in the Ankara 2008 classification criteria for GPA is the presence of nodules, cavities, or fixed infiltrates. The adult data suggest that rituximab may be an alternative to cyclophosphamide in induction treatment.

Identifiants

pubmed: 33228930
pii: S0031-3955(20)30136-X
doi: 10.1016/j.pcl.2020.09.014
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

167-176

Informations de copyright

Copyright © 2020 Elsevier Inc. All rights reserved.

Déclaration de conflit d'intérêts

Disclosure The authors have nothing to disclose related to this work. However, Dr S. Ozen has received consultation and speaker fees from Novartis and SOBI.

Auteurs

Muserref Kasap Cuceoglu (MK)

Department of Pediatric Rheumatology, Hacettepe University, Sihhiye Campus, Ankara 06100, Turkey.

Seza Ozen (S)

Department of Pediatric Rheumatology, Hacettepe University, Sihhiye Campus, Ankara 06100, Turkey. Electronic address: sezaozen@gmail.com.

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Classifications MeSH