Bilateral symmetric lipomatosis of the orbit in Madelung's disease.
Benign symmetric lipomatosis
Launois-Bensaude syndrome
Madelung’s disease
Journal
Orbit (Amsterdam, Netherlands)
ISSN: 1744-5108
Titre abrégé: Orbit
Pays: England
ID NLM: 8301221
Informations de publication
Date de publication:
Apr 2022
Apr 2022
Historique:
pubmed:
28
11
2020
medline:
19
3
2022
entrez:
27
11
2020
Statut:
ppublish
Résumé
Madelung's disease is a rare benign systemic lipomatosis, which often presents in the head, neck and upper trunk regions. The appearance of symmetrical, excessive adipose tissue in the subcutaneous layer is its clinical characteristic. Orbital involvement is unusual with only a few cases reported previously. In this study, we describe the clinical and radiological features of Madelung's disease in the orbits. A 42-year-old man with alcohol addiction presented with chronic bilateral masses of the lower eyelids and proptosis. Computed tomography (CT) scan showed excessive symmetrical non-encapsulated fat deposition in the orbital fat, lower eyelids, salivary glands, subcutaneous tissue along the neck and under the sternocleidomastoid muscles and supraclavicular areas bilaterally. Histopathological study of the orbital masses revealed mature adipose tissue interspersed with thin fibrous septae. He developed recurrent lipomatosis 1 year after surgical excision.
Identifiants
pubmed: 33243058
doi: 10.1080/01676830.2020.1852261
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM