Fourth Ventricle Outlet Obstruction and Diverticular Enlargement of Luschka Foramina in a Child with Down Syndrome.
Down syndrome
Endoscopic third ventriculostomy
Fourth ventricle outlet obstruction
Hydrocephalus
Ventricular diverticulum
Journal
Pediatric neurosurgery
ISSN: 1423-0305
Titre abrégé: Pediatr Neurosurg
Pays: Switzerland
ID NLM: 9114967
Informations de publication
Date de publication:
2020
2020
Historique:
received:
24
03
2020
accepted:
24
08
2020
pubmed:
29
12
2020
medline:
29
10
2021
entrez:
28
12
2020
Statut:
ppublish
Résumé
Hydrocephalus is not usually part of Down syndrome (DS). Fourth ventricle outlet obstruction is a rare cause of obstructive hydrocephalus, difficult to diagnose, because tetraventricular dilatation may suggest a communicant/nonobstructive hydrocephalus. We describe the case of a 6-year-old boy with obstructive tetraventricular hydrocephalus, caused by Luschka and Magen-die foramina obstruction and diverticular enlargement of Luschka foramina (the so-called fourth ventricle outlet obstruction) associated with DS. He was treated with endoscopic third ventriculostomy (ETV) without complications, and a follow-up MRI revealed reduction of the ventricles, disappearance of the diverticula, and patency of the ventriculostomy. Diverticular enlargement of Luschka foramina is an important radiological finding for obstructive tetraventricular hydrocephalus. ETV is a viable option in tetraventricular obstructive hydrocephalus in DS.
Identifiants
pubmed: 33370726
pii: 000511088
doi: 10.1159/000511088
doi:
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
359-362Informations de copyright
© 2020 S. Karger AG, Basel.