Gorham Stout disease: a case report from Syria.

Gorham Stout disease angiomatosis lytic bone disease osteolysis vanishing bone disease

Journal

Oxford medical case reports
ISSN: 2053-8855
Titre abrégé: Oxf Med Case Reports
Pays: England
ID NLM: 101642070

Informations de publication

Date de publication:
Jan 2021
Historique:
received: 14 07 2020
revised: 13 10 2020
accepted: 31 10 2020
entrez: 20 1 2021
pubmed: 21 1 2021
medline: 21 1 2021
Statut: epublish

Résumé

Gorham-Stout disease (GSD) is a rare entity that destroys the bone matrix resulting mainly in osteolysis, pain and pathologic fractures among a broader clinical picture. We report a case of a 60-year-old female with a sudden discovery of pathologic fractures in the pelvis and the absence of the left femoral head. On biopsy, no cellular atypia was found, instead disturbed bone formation with prominent vascularity with scattered foci of necrosis & osteolysis, which lead to the diagnosis of GSD. Possible differential diagnoses were discussed and excluded. The patient was put on Bisphosphonate that led to a relative improvement in the symptoms. This disease needs a more thorough investigation to identify the key cause, what is beyond the scope of this report.

Identifiants

pubmed: 33469472
doi: 10.1093/omcr/omaa121
pii: omaa121
pmc: PMC7802812
doi:

Types de publication

Case Reports

Langues

eng

Pagination

omaa121

Informations de copyright

© The Author(s) 2020. Published by Oxford University Press. All rights reserved. For Permissions, please email: journals.permissions@oup.com.

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Auteurs

Asil Esper (A)

Neurology Department, Tishreen University Hospital, Halap street, Latakia, Syria.

Sami Alhoulaiby (S)

Faculty of Medicine, Damascus University, Damascus, Syria.

Areege Emran (A)

Pulmonary Department, Tishreen University Hospital, Latakia, Syria.

Safwan Youssef (S)

Orthopedics Department, Tishreen University Hospital, Latakia, Syria.

Zuheir Alshehabi (Z)

Pathology Department, Tishreen University Hospital, Latakia, Syria.

Classifications MeSH