Galactose treatment of a PGM1 patient presenting with restrictive cardiomyopathy.

PGM1‐CDG galactose restrictive cardiomyopathy

Journal

JIMD reports
ISSN: 2192-8304
Titre abrégé: JIMD Rep
Pays: United States
ID NLM: 101568557

Informations de publication

Date de publication:
Jan 2021
Historique:
received: 03 08 2020
revised: 11 10 2020
accepted: 13 10 2020
entrez: 21 1 2021
pubmed: 22 1 2021
medline: 22 1 2021
Statut: epublish

Résumé

We report a patient diagnosed with PGM1-CDG at 11 years of age after two biallelic likely pathogenic variants in

Identifiants

pubmed: 33473337
doi: 10.1002/jmd2.12177
pii: JMD212177
pmc: PMC7802629
doi:

Types de publication

Case Reports

Langues

eng

Pagination

29-37

Informations de copyright

© 2020 The Authors. JIMD Reports published by John Wiley & Sons Ltd on behalf of SSIEM.

Déclaration de conflit d'intérêts

Sarah Donoghue, Susan White, Tiong Tan, Remi Kowalski, Eva Morava and Joy Yaplito‐Lee declare that they have no conflict of interest.

Références

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Auteurs

Sarah E Donoghue (SE)

Department of Metabolic Medicine Royal Children's Hospital Melbourne Victoria Australia.
Victorian Clinical Genetics Services Murdoch Children's Research Institute Melbourne Victoria Australia.

Susan M White (SM)

Victorian Clinical Genetics Services Murdoch Children's Research Institute Melbourne Victoria Australia.
Department of Paediatrics University of Melbourne Melbourne Victoria Australia.

Tiong Yang Tan (TY)

Victorian Clinical Genetics Services Murdoch Children's Research Institute Melbourne Victoria Australia.
Department of Paediatrics University of Melbourne Melbourne Victoria Australia.

Remi Kowalski (R)

Department of Cardiology Royal Children's Hospital Melbourne Victoria Australia.

Eva Morava (E)

Department of Clinical Genomics Mayo Clinic Rochester Minnesota USA.
Department of Pediatrics University Hospitals Leuven Leuven Belgium.

Joy Yaplito-Lee (J)

Department of Metabolic Medicine Royal Children's Hospital Melbourne Victoria Australia.
Department of Paediatrics University of Melbourne Melbourne Victoria Australia.

Classifications MeSH