Patient iPSC-derived retinal organoids: Observable retinal diseases in-a-dish.


Journal

Histology and histopathology
ISSN: 1699-5848
Titre abrégé: Histol Histopathol
Pays: Spain
ID NLM: 8609357

Informations de publication

Date de publication:
Jul 2021
Historique:
pubmed: 26 1 2021
medline: 2 2 2022
entrez: 25 1 2021
Statut: ppublish

Résumé

Induced pluripotent stem cells (iPSCs), reprogrammed from human somatic cells, hold the capacity to differentiate into most human body cells. iPSCs can be differentiated into retinal organoids, a three-dimensional structured retina containing various retinal cells. Patient-specific retinal organoids provide a powerful disease model to recapitulate the disease to study the pathogenesis of inherited retinal dystrophies, to screen or discover new drugs, and most importantly to supply an unlimited cell source for retinal regeneration.

Identifiants

pubmed: 33491763
pii: HH-18-307
doi: 10.14670/HH-18-307
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

705-710

Subventions

Organisme : Beijing Natural Science Foundation
ID : Z200014
Organisme : National Key RandD Program of China
ID : 2017YFA0105300

Références

Achberger K., Haderspeck J.C., Kleger A. and Liebau S. (2019a). Stem cell-based retina models. Adv. Drug Deliv. Rev. 140, 33-50.
pubmed: 29777757
Achberger K., Probst C., Haderspeck J., Bolz S., Rogal J., Chuchuy J., Nikolova M., Cora V., Antkowiak L., Haq W., Shen N., Schenke- Layland K., Ueffing M., Liebau S. and Loskill P. (2019b). Merging organoid and organ-on-a-chip technology to generate complex multilayer tissue models in a human retina-on-a-chip platform. Elife 8, e46188.
pmcid: PMC6777939 pubmed: 31451149
Artero Castro A., Long K., Bassett A., Machuca C., León M., Ávila- Fernandez A., Cortón M., Vidal-Puig T., Ayuso C., Lukovic D. and Erceg S. (2019). Generation of gene-corrected human induced pluripotent stem cell lines derived from retinitis pigmentosa patient with Ser331Cysfs*5 mutation in Mertk. Stem Cell Res. 34, 101341.
pubmed: 30612079
Avior Y., Sagi I. and Benvenisty N. (2016). Pluripotent stem cells in disease modelling and drug discovery. Nat. Rev. Mol. Cell Biol. 17, 170-182.
pubmed: 26818440
Bakondi B., Lv W., Lu B., Jones M.K., Tsai Y., Kim K. J., Levy R., Akhtar A.A., Breunig J.J., Svendsen C.N. and Wang S. (2016). In vivo CRISPR/cas9 gene editing corrects retinal dystrophy in the S334ter- 3 rat model of autosomal dominant retinitis pigmentosa. Mol. Ther. 24, 556-563.
pmcid: PMC4786918 pubmed: 26666451
Bassuk A.G., Zheng A., Li Y., Tsang S.H. and Mahajan V.B. (2016). Precision medicine: genetic repair of retinitis pigmentosa in patientderived stem cells. Sci. Rep. 6, 19969.
pmcid: PMC4728485 pubmed: 26814166
Burnight E.R., Gupta M., Wiley L.A., Anfinson K.R., Tran A., Triboulet R., Hoffmann J.M., Klaahsen D.L., Andorf J.L., Jiao C., Sohn E.H., Adur M.K., Ross J. W., Mullins R.F., Daley G.Q., Schlaeger T.M., Stone E.M. and Tucker B.A. (2017). Using CRISPR-cas9 to generate gene-corrected autologous iPSCs for the treatment of inherited retinal degeneration. Mol. Ther. 25, 1999-2013.
pmcid: PMC5589061 pubmed: 28619647
Buskin A., Zhu L., Chichagova V., Basu B., Mozaffari-Jovin S., Dolan D., Droop A., Collin J., Bronstein R., Mehrotra S., Farkas M., Hilgen G., White K., Pan K.T., Treumann A., Hallam D., Bialas K., Chung G., Mellough C., Ding Y., Krasnogor N., Przyborski S., Zwolinski S., Al- Aama J., Alharthi S., Xu Y., Wheway G., Szymanska K., McKibbin M., Inglehearn C.F., Elliott D.J., Lindsay S., Ali R.R., Steel D.H., Armstrong L., Sernagor E., Urlaub H., Pierce E., Lührmann R., Grellscheid S.N., Johnson C.A. and Lako M. (2018). Disrupted alternative splicing for genes implicated in splicing and ciliogenesis causes PRPF31 retinitis pigmentosa. Nat. Commun. 9, 4234.
pmcid: PMC6185938 pubmed: 30315276
Deng W.L., Gao M.L., Lei X.L., Lv J.N., Zhao H., He K.W., Xia X.X., Li L.Y., Chen Y.C., Li Y.P., Pan D., Xue T. and Jin Z.B. (2018). Gene correction reverses ciliopathy and photoreceptor loss in iPSCderived retinal organoids from retinitis pigmentosa patients. Stem Cell Rep. 10, 1267-1281.
pmcid: PMC5998840 pubmed: 29526738
Dimaras H., Kimani K., Dimba E.A., Gronsdahl P., White A., Chan H.S. and Gallie B.L. (2012). Retinoblastoma. Lancet 379, 1436-1446.
pubmed: 22414599
Eiraku M., Takata N., Ishibashi H., Kawada M., Sakakura E., Okuda S., Sekiguchi K., Adachi T. and Sasai Y. (2011). Self-organizing opticcup morphogenesis in three-dimensional culture. Nature 472, 51-56.
pubmed: 21475194
Friend S.H., Bernards R., Rogelj S., Weinberg R.A., Rapaport J.M., Albert D.M. and Dryja T.P. (1986). A human DNA segment with properties of the gene that predisposes to retinoblastoma and osteosarcoma. Nature 323, 643-646.
pubmed: 2877398
Gao M.L., Lei X.L., Han F., He K.W., Jin S.Q., Zhang Y.Y. and Jin Z.B. (2020). Patient-specific retinal organoids recapitulate disease features of late-onset retinitis pigmentosa. Front. Cell Dev. Biol. 8, 128.
pmcid: PMC7068133 pubmed: 32211407
Ghazi N.G., Abboud E.B., Nowilaty S.R., Alkuraya H., Alhommadi A., Cai H., Hou R., Deng W.T., Boye S.L., Almaghamsi A., Al Saikhan F., Al-Dhibi H., Birch D., Chung C., Colak D., LaVail M.M., Vollrath D., Erger K., Wang W., Conlon T., Zhang K., Hauswirth W. and Alkuraya F.S. (2016). Treatment of retinitis pigmentosa due to Mertk mutations by ocular subretinal injection of adeno-associated virus gene vector: results of a phase I trial. Hum. Genet. 135, 327-343.
pubmed: 26825853
Guo Y., Wang P., Ma J.H., Cui Z., Yu Q., Liu S., Xue Y., Zhu D., Cao J., Li Z., Tang S. and Chen J. (2019). Modeling retinitis pigmentosa: retinal organoids generated from the iPSCs of a patient with the USH2A mutation show early developmental abnormalities. Front. Cell. Neurosci. 13, 361.
pmcid: PMC6709881 pubmed: 31481876
Jin Z.B. and Takahashi M. (2012). Generation of retinal cells from pluripotent stem cells. Prog. Brain Res. 201, 171-181.
pubmed: 23186714
Jin Z.B., Okamoto S., Mandai M. and Takahashi M. (2009). Induced pluripotent stem cells for retinal degenerative diseases: a new perspective on the challenges. J. Genet. 88, 417-424.
pubmed: 20090205
Jin Z.B., Okamoto S., Osakada F., Homma K., Assawachananont J., Hirami Y., Iwata T. and Takahashi M. (2011). Modeling retinal degeneration using patient-specific induced pluripotent stem cells. PLoS One 6, e17084.
pmcid: PMC3037398 pubmed: 21347327
Jin Z.B., Okamoto S., Xiang P. and Takahashi M. (2012). Integrationfree induced pluripotent stem cells derived from retinitis pigmentosa patient for disease modeling. Stem Cells Transl. Med. 1, 503- 509.
pmcid: PMC3659711 pubmed: 23197854
Jin Z.B., Gao M.L., Deng W.L., Wu K.C., Sugita S., Mandai M. and Takahashi M. (2019). Stemming retinal regeneration with pluripotent stem cells. Prog. Retin. Eye Res. 69, 38-56.
pubmed: 30419340
Li G., Gao G., Wang P., Song X., Xu P., Xie B., Zhou T., Pan G., Peng F., Zhang Q., Ge J. and Zhong X. (2019). Generation and characterization of induced pluripotent stem cells and retinal organoids from a Leber’s Congenital Amaurosis patient with novel RPE65 mutations. Front. Mol. Neurosci. 12, 212.
pmcid: PMC6749091 pubmed: 31572124
Liu H., Zhang Y., Zhang Y.Y., Li Y.P., Hua Z.Q., Zhang C.J., Wu K.C., Yu F., Zhang Y., Su J. and Jin Z.B. (2020). Human embryonic stem cell-derived organoid retinoblastoma reveals a cancerous origin. Proc. Natl. Acad. Sci. USA 117, 33628-33638.
pmcid: PMC7776986 pubmed: 33318192
Lukovic D., Artero Castro A., Delgado A.B., Bernal Mde L., Luna Pelaez N., Díez Lloret A., Perez Espejo R., Kamenarova K., Fernández Sánchez L., Cuenca N., Cortón M., Avila Fernandez A., Sorkio A., Skottman H., Ayuso C., Erceg S. and Bhattacharya S.S. (2015). Human iPSC derived disease model of MERTK-associated retinitis pigmentosa. Sci. Rep. 5, 12910.
pmcid: PMC4531787 pubmed: 26263531
Lukovic D., Artero Castro A., Kaya K.D., Munezero D., Gieser L., Davó- Martínez C., Corton M., Cuenca N., Swaroop A., Ramamurthy V., Ayuso C. and Erceg S. (2020). Retinal organoids derived from hiPSCs of an AIPL1-LCA patient maintain cytoarchitecture despite reduced levels of mutant AIPL1. Sci. Rep. 10, 5426.
pmcid: PMC7096529 pubmed: 32214115
Pan D., Xia X.X., Zhou H., Jin S.Q., Lu Y.Y., Liu H., Gao M.L. and Jin Z.B. (2020). COCO enhances the efficiency of photoreceptor precursor differentiation in early human embryonic stem cell-derived retinal organoids. Stem Cell Res. Ther. 11, 366.
pmcid: PMC7444242 pubmed: 32831148
Parfitt D.A., Lane A., Ramsden C.M., Carr A.J., Munro P.M., Jovanovic K., Schwarz N., Kanuga N., Muthiah M.N., Hull S., Gallo J.M., da Cruz L., Moore A.T., Hardcastle A.J., Coffey P.J. and Cheetham M.E. (2016). Identification and correction of mechanisms underlying inherited blindness in human iPSC-derived optic cups. Cell Stem Cell 18, 769-781.
pmcid: PMC4899423 pubmed: 27151457
Pausch P., Al-Shayeb B., Bisom-Rapp E., Tsuchida C.A., Li Z., Cress B.F., Knott G. J., Jacobsen S.E., Banfield J.F. and Doudna J.A. (2020). CRISPR-CasΦ from huge phages is a hypercompact genome editor. Science 369, 333-337.
pmcid: PMC8207990 pubmed: 32675376
Ran X., Cai W.J., Huang X.F., Liu Q., Lu F., Qu J., Wu J.Y. and Jin Z.B. (2014). 'RetinoGenetics': a comprehensive mutation database for genes related to inherited retinal degeneration. Database. 2014, bau047.
pmcid: PMC4060621 pubmed: 24939193
Sanjurjo-Soriano C., Erkilic N., Baux D., Mamaeva D., Hamel C.P., Meunier I., Roux A.F. and Kalatzis V. (2020). Genome editing in patient iPSCs corrects the most prevalent USH2A mutations and reveals intriguing mutant mRNA expression profiles. Mol. Ther. Methods Clin. Dev. 17, 156-173.
pmcid: PMC6938853 pubmed: 31909088
Shimada H., Lu Q., Insinna-Kettenhofen C., Nagashima K., English M.A., Semler E.M., Mahgerefteh J., Cideciyan A.V., Li T., Brooks B.P., Gunay-Aygun M., Jacobson S.G., Cogliati T., Westlake C.J. and Swaroop A. (2017). In vitro modeling using ciliopathy-patientderived cells reveals distinct cilia dysfunctions caused by CEP290 mutations. Cell Rep. 20, 384-396.
pmcid: PMC5553702 pubmed: 28700940
Sugita S., Iwasaki Y., Makabe K., Kamao H., Mandai M., Shiina T., Ogasawara K., Hirami Y., Kurimoto Y. and Takahashi M. (2016). Successful transplantation of retinal pigment epithelial cells from MHC homozygote iPSCs in MHC-matched models. Stem Cell Rep. 7, 635-648.
pmcid: PMC5063629 pubmed: 27641649
Tang Z.H., Chen J.R., Zheng J., Shi H.S., Ding J., Qian X.D., Zhang C., Chen J.L., Wang C.C., Li L., Chen J.Z., Yin S.K., Huang T.S., Chen P., Guan M.X. and Wang J.F. (2016). Genetic correction of induced pluripotent stem cells from a deaf patient with MYO7A mutation results in morphologic and functional recovery of the derived hair cell-like cells. Stem Cells Transl. Med. 5, 561-571.
pmcid: PMC4835250 pubmed: 27013738
Tsang S.H. and Sharma T. (2018). Leber congenital amaurosis. Adv. Exp. Med. Biol. 1085, 131-137.
pubmed: 30578499
Tucker B.A., Mullins R.F., Streb L.M., Anfinson K., Eyestone M.E., Kaalberg E., Riker M.J., Drack A.V., Braun T.A. and Stone E.M. (2013). Patient-specific iPSC-derived photoreceptor precursor cells as a means to investigate retinitis pigmentosa. Elife 2, e00824.
pmcid: PMC3755341 pubmed: 23991284
Wahlin K.J., Maruotti J.A., Sripathi S.R., Ball J., Angueyra J.M., Kim C., Grebe R., Li W., Jones B.W. and Zack D.J. (2017). Photoreceptor outer segment-like structures in long-term 3D retinas from human pluripotent stem cells. Sci. Rep. 7, 766.
pmcid: PMC5429674 pubmed: 28396597
Zhang J.P., Li X.L., Li G.H., Chen W., Arakaki C., Botimer G.D., Baylink D., Zhang L., Wen W., Fu Y.W., Xu J., Chun N., Yuan W., Cheng T. and Zhang X.B. (2017). Efficient precise knockin with a double cut HDR donor after CRISPR/Cas9-mediated double-stranded DNA cleavage. Genome Biol. 18, 35.
pmcid: PMC5319046 pubmed: 28219395
Zhang C.J., Ma Y. and Jin Z.B. (2021). The road to restore vision with photoreceptor regeneration. Exp. Eye Res. 202, 108283.
pubmed: 33010290
Zhong X., Gutierrez C., Xue T., Hampton C., Vergara M.N., Cao L.H., Peters A., Park T.S., Zambidis E.T., Meyer J.S., Gamm D.M., Yau K.W. and Canto-Soler M.V. (2014). Generation of three-dimensional retinal tissue with functional photoreceptors from human iPSCs. Nat. Commun. 5, 4047.
pmcid: PMC4370190 pubmed: 24915161

Auteurs

Xiao-Hui Zhang (XH)

Beijing Institute of Ophthalmology, Beijing Tongren Eye Center, Beijing Tongren Hospital, Capital Medical University, Beijing Ophthalmology and Visual Sciences Key Laboratory, Beijing, China.

Zi-Bing Jin (ZB)

Beijing Institute of Ophthalmology, Beijing Tongren Eye Center, Beijing Tongren Hospital, Capital Medical University, Beijing Ophthalmology and Visual Sciences Key Laboratory, Beijing, China. jinzb502@ccmu.edu.cn.

Articles similaires

[Redispensing of expensive oral anticancer medicines: a practical application].

Lisanne N van Merendonk, Kübra Akgöl, Bastiaan Nuijen
1.00
Humans Antineoplastic Agents Administration, Oral Drug Costs Counterfeit Drugs

Smoking Cessation and Incident Cardiovascular Disease.

Jun Hwan Cho, Seung Yong Shin, Hoseob Kim et al.
1.00
Humans Male Smoking Cessation Cardiovascular Diseases Female
Humans United States Aged Cross-Sectional Studies Medicare Part C
1.00
Humans Yoga Low Back Pain Female Male

Classifications MeSH