Genotype to Phenotype: Identification of Mucopolysaccharidosis Type IIIB (Sanfilippo's B) Case Using Whole Exome Sequencing.

Sanfilippo's syndrome B consanguineous marriage mucopolysaccharidosis III whole exome sequencing

Journal

Journal of pediatric genetics
ISSN: 2146-4596
Titre abrégé: J Pediatr Genet
Pays: Germany
ID NLM: 101589859

Informations de publication

Date de publication:
Mar 2021
Historique:
received: 21 10 2019
accepted: 13 02 2020
entrez: 8 2 2021
pubmed: 9 2 2021
medline: 9 2 2021
Statut: ppublish

Résumé

Mucopolysaccharidosis type IIIB (Sanfilippo's B; OMIM no.: 252920) is a lysosomal storage disorder caused by defective degradation of heparan sulfate. The enzyme that has decreased function in this disease is α-N acetylglucosaminidase. This enzyme is encoded by the

Identifiants

pubmed: 33552644
doi: 10.1055/s-0040-1708555
pii: 1900094
pmc: PMC7853908
doi:

Types de publication

Case Reports

Langues

eng

Pagination

74-76

Informations de copyright

Thieme. All rights reserved.

Déclaration de conflit d'intérêts

Conflict of Interest None declared.

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Auteurs

Muhsin Elmas (M)

Medical Genetics Department, Afyonkarahisar Health Sciences University, Afyonkarahisar, Turkey.

Basak Gogus (B)

Medical Genetics Department, Afyonkarahisar Health Sciences University, Afyonkarahisar, Turkey.

Furkan Kılıçarslan (F)

Faculty of Arts and Sciences, Genetics & Bioinformatics, Bahcesehir University, Istanbul, Turkey.

Aysegul Bukulmez (A)

Pediatry Department, Afyonkarahisar Health Sciences University, Afyonkarahisar, Turkey.

Mustafa Solak (M)

Medical Genetics Department, Afyonkarahisar Health Sciences University, Afyonkarahisar, Turkey.

Classifications MeSH