Tissue is the issue: when a second biopsy reveals the true diagnosis.

collagen IV nephropathies focal segmental glomerulosclerosis gene expression glomerulonephritis

Journal

Clinical kidney journal
ISSN: 2048-8505
Titre abrégé: Clin Kidney J
Pays: England
ID NLM: 101579321

Informations de publication

Date de publication:
Jan 2021
Historique:
received: 30 07 2019
accepted: 22 10 2019
entrez: 10 2 2021
pubmed: 10 12 2019
medline: 10 12 2019
Statut: epublish

Résumé

We describe the case of a woman with minimal glomerular changes on initial kidney biopsy. On long-term follow-up, the patient developed nephrotic proteinuria and a second kidney biopsy was performed, which revealed focal segmental glomerulosclerosis (FSGS). Findings from electron microscopy (EM) examination suggested a genetic form of FSGS. Next-generation sequencing showed heterozygosity for a mutation in

Identifiants

pubmed: 33564449
doi: 10.1093/ckj/sfz165
pii: sfz165
pmc: PMC7857801
doi:

Types de publication

Case Reports

Langues

eng

Pagination

429-431

Informations de copyright

© The Author(s) 2019. Published by Oxford University Press on behalf of ERA-EDTA.

Références

Clin Kidney J. 2017 Oct;10(5):586-593
pubmed: 28980669
Nephron. 2015;130(4):271-80
pubmed: 26201269
J Am Soc Nephrol. 2018 Mar;29(3):759-774
pubmed: 29321142
Nephrol Dial Transplant. 2016 Jun;31(6):961-70
pubmed: 26346198
Clin Kidney J. 2018 Apr;11(2):179-190
pubmed: 29644057

Auteurs

Anne-Marie Bogaert (AM)

Department of Nephrology, AZ Sint-Elisabeth, Zottegem, Belgium.

Anne Hoorens (A)

Department of Pathology, Ghent University Hospital, Ghent, Belgium.

Marleen Praet (M)

Department of Pathology, Ghent University Hospital, Ghent, Belgium.

Jo Van Dorpe (J)

Department of Pathology, Ghent University Hospital, Ghent, Belgium.

Bruce Poppe (B)

Center for Medical Genetics, Ghent University Hospital, Ghent, Belgium.

Marie-Angélique De Scheerder (MA)

Department of Internal Medicine, Ghent University Hospital, Ghent, Belgium.

Classifications MeSH