Case Report: Efficacy of Rituximab in a Patient With Familial Mediterranean Fever and Multiple Sclerosis.

case report familal mediterranean fever hepatotoxicity multiple sclerosis rituximab

Journal

Frontiers in neurology
ISSN: 1664-2295
Titre abrégé: Front Neurol
Pays: Switzerland
ID NLM: 101546899

Informations de publication

Date de publication:
2020
Historique:
received: 04 08 2020
accepted: 04 12 2020
entrez: 15 2 2021
pubmed: 16 2 2021
medline: 16 2 2021
Statut: epublish

Résumé

Familial Mediterranean Fever (FMF) is a genetic autoinflammatory disease characterized by recurrent episodes of fever and serositis caused by mutations in the MEFV gene, while Multiple Sclerosis (MS) is an inflammatory demyelinating disease of the CNS with genetic and environmental etiology. The two diseases rarely occur in association with relevant implications for clinical management and drug choice. In this paper, we present the case of a 53-year-old male with an autosomal dominant FMF since childhood who presented acute paresthesia at the right part of the body. He performed a brain and spinal cord MRI, which showed multiple brain lesions and a gd-enhancing lesion in the cervical spinal cord, and then received a diagnosis of MS. He then started Interferonβ-1a which was effective but not tolerated and caused hepatotoxicity, and then shifted to Rituximab with 3-month clinical and neuroradiological efficacy.

Identifiants

pubmed: 33584496
doi: 10.3389/fneur.2020.591395
pmc: PMC7874168
doi:

Types de publication

Case Reports

Langues

eng

Pagination

591395

Informations de copyright

Copyright © 2021 Pozzato, Micaglio, Starvaggi Cucuzza, Cagol, Galimberti, Calandrella, Cinnante, Pappone, Zanussi, Meola, Scarpini, Bresolin and Martinelli Boneschi.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Mattia Pozzato (M)

Foundation Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Ca' Granda Ospedale Maggiore Policlinico, Neurology Unit & MS Centre, Milan, Italy.
Neuroscience Section, Department of Pathophysiology and Transplantation (DEPT), Dino Ferrari Centre, University of Milan, Milan, Italy.

Emanuele Micaglio (E)

Arrhythmology and Electrophysiology Department, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Milan, Italy.

Chiara Starvaggi Cucuzza (C)

Department of Neurology, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, San Donato Milanese, Italy.

Alessandro Cagol (A)

Department of Neurology, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, San Donato Milanese, Italy.

Daniela Galimberti (D)

Department of Biomedical, Surgical and Dental Sciences, Dino Ferrari Centre, University of Milan, Milan, Italy.

Daniela Calandrella (D)

Department of Neurology, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Humanitas Research Hospital and University, Milan, Italy.

Claudia Cinnante (C)

Neuroradiology Unit, Foundation Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy.

Carlo Pappone (C)

Arrhythmology and Electrophysiology Department, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Milan, Italy.

Monica Zanussi (M)

Clinical Genomics-Molecular Genetics Service, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, San Raffaele Hospital, Milan, Italy.

Giovanni Meola (G)

Department of Biomedical Sciences for Health, University of Milan, Milan, Italy.
Department of Neurorehabilitation Sciences, Casa di Cura Privata del Policlinico, Milan, Italy.

Elio Scarpini (E)

Foundation Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Ca' Granda Ospedale Maggiore Policlinico, Neurology Unit & MS Centre, Milan, Italy.
Department of Biomedical, Surgical and Dental Sciences, Dino Ferrari Centre, University of Milan, Milan, Italy.

Nereo Bresolin (N)

Foundation Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Ca' Granda Ospedale Maggiore Policlinico, Neurology Unit & MS Centre, Milan, Italy.
Neuroscience Section, Department of Pathophysiology and Transplantation (DEPT), Dino Ferrari Centre, University of Milan, Milan, Italy.

Filippo Martinelli Boneschi (F)

Foundation Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Policlinico San Donato, Ca' Granda Ospedale Maggiore Policlinico, Neurology Unit & MS Centre, Milan, Italy.
Neuroscience Section, Department of Pathophysiology and Transplantation (DEPT), Dino Ferrari Centre, University of Milan, Milan, Italy.

Classifications MeSH