An AIREless Breath: Pneumonitis Caused by Impaired Central Immune Tolerance.

Autoimmune-polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED) autoimmune polyglandular syndrome type-1 (APS-1) autoimmune regulator (AIRE) bronchiectasis interstitial lung disease pneumonitis

Journal

Frontiers in immunology
ISSN: 1664-3224
Titre abrégé: Front Immunol
Pays: Switzerland
ID NLM: 101560960

Informations de publication

Date de publication:
2020
Historique:
received: 22 09 2020
accepted: 01 12 2020
entrez: 15 2 2021
pubmed: 16 2 2021
medline: 24 6 2021
Statut: epublish

Résumé

Autoimmune-polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED), a monogenic disorder caused by biallelic mutations in the

Identifiants

pubmed: 33584685
doi: 10.3389/fimmu.2020.609253
pmc: PMC7873437
doi:

Substances chimiques

Transcription Factors 0

Types de publication

Journal Article Research Support, N.I.H., Intramural Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

609253

Informations de copyright

Copyright © 2021 Ferré and Lionakis.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Elise M N Ferré (EMN)

Fungal Pathogenesis Section, Laboratory of Clinical Immunology and Microbiology, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, United States.

Michail S Lionakis (MS)

Fungal Pathogenesis Section, Laboratory of Clinical Immunology and Microbiology, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, United States.

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