Mycosis Fungoides with Dermal Mucin Deposition: An Unusual Variant of the Most Challenging Primary Cutaneous Lymphoma.

Cutaneous T-cell lymphoma Mucin Mycosis fungoides

Journal

Case reports in dermatology
ISSN: 1662-6567
Titre abrégé: Case Rep Dermatol
Pays: Switzerland
ID NLM: 101517685

Informations de publication

Date de publication:
Historique:
received: 05 04 2020
accepted: 17 06 2020
entrez: 22 2 2021
pubmed: 23 2 2021
medline: 23 2 2021
Statut: epublish

Résumé

Mycosis fungoides (MF) is defined as an epidermotropic primary cutaneous T-cell lymphoma composed of small-to-medium-sized T lymphocytes with cerebriform nuclei and with a T-helper phenotype. LeBoit first described an unusual variant of MF with dermal acid mucin deposition. Such a variant was still considered in the list of clinicopathological variants of MF by Cerroni and colleagues. We herein report a case of patch-stage MF with abundant papillary dermal mucin deposition in a clinical setting of an erythematous patch on the lower abdomen and thigh.

Identifiants

pubmed: 33613227
doi: 10.1159/000509525
pii: cde-0013-0007
pmc: PMC7879304
doi:

Types de publication

Case Reports

Langues

eng

Pagination

7-11

Informations de copyright

Copyright © 2021 by S. Karger AG, Basel.

Déclaration de conflit d'intérêts

The authors declare no conflicts of interest.

Références

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pubmed: 26009972
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Auteurs

Alessandra Filosa (A)

Pathology Unit, Azienda Sanitaria Unica Regionale Area Vasta 5 Ospedale G. Mazzoni, Ascoli Piceno, Italy.

Stefano Simonetti (S)

Dermatology Unit, Ospedale Santa Maria della Misericordia, University of Perugia, Perugia, Italy.

Magda Zanelli (M)

Pathology Unit, Azienda Unità Sanitaria Locale/IRCCS di Reggio Emilia, Reggio Emilia, Italy.

Maurizio Zizzo (M)

Surgical Oncology Unit, Azienda Unità Sanitaria Locale - IRCCS di Reggio Emilia, Reggio Emilia, Italy.

Luca Stingeni (L)

Dermatology Unit, Ospedale Santa Maria della Misericordia, University of Perugia, Perugia, Italy.

Giovanni Martino (G)

Institute of Hematology-CREO, Ospedale Santa Maria della Misericordia, University of Perugia, Perugia, Italy.

Guido Collina (G)

Pathology Unit, Azienda Sanitaria Unica Regionale Area Vasta 5 Ospedale G. Mazzoni, Ascoli Piceno, Italy.

Stefano Ascani (S)

Pathology Unit, Ospedale di Terni, University of Perugia, Terni, Italy.

Classifications MeSH