Rhabdoid Tumor Predisposition Syndrome: From Clinical Suspicion to General Management.

atypical teratoid/rhabdoid tumors cancer predisposition syndromes cancer risk cancer surveillance genetic test rhabdoid tumors

Journal

Frontiers in oncology
ISSN: 2234-943X
Titre abrégé: Front Oncol
Pays: Switzerland
ID NLM: 101568867

Informations de publication

Date de publication:
2021
Historique:
received: 22 07 2020
accepted: 05 01 2021
entrez: 11 3 2021
pubmed: 12 3 2021
medline: 12 3 2021
Statut: epublish

Résumé

Rhabdoid tumors are rare aggressive malignancies in infants and young children with a poor prognosis. The most common anatomic localizations are the central nervous system, the kidneys, and other soft tissues. Rhabdoid tumors share germline and somatic mutations in

Identifiants

pubmed: 33692948
doi: 10.3389/fonc.2021.586288
pmc: PMC7937887
doi:

Types de publication

Journal Article Review

Langues

eng

Pagination

586288

Informations de copyright

Copyright © 2021 Del Baldo, Carta, Alessi, Merli, Agolini, Rinelli, Boccuto, Milano, Serra, Carai, Locatelli and Mastronuzzi.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Giada Del Baldo (G)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Roberto Carta (R)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Iside Alessi (I)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Pietro Merli (P)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Emanuele Agolini (E)

Laboratory of Medical Genetics, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Martina Rinelli (M)

Laboratory of Medical Genetics, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Luigi Boccuto (L)

JC Self Research Institute, Greenwood Genetic Center, Greenwood, SC, United States.
School of Nursing, College of Behavioral, Social and Health Science, Clemson University, Clemson, SC, United States.

Giuseppe Maria Milano (GM)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Annalisa Serra (A)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Andrea Carai (A)

Department of Neuroscience and Neurorehabilitation, Neurosurgery Unit, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Franco Locatelli (F)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.
Department of Maternal, Infantile, and Urological Sciences, University of Rome La Sapienza, Rome, Italy.

Angela Mastronuzzi (A)

Department of Paediatric Haematology/Oncology, IRCCS Bambino Gesù Children's Hospital, Rome, Italy.

Classifications MeSH