Portosystemic shunt with hyperammonemia and high cardiac output as a complication after Fontan surgery.

Fontan-associated liver disease High cardiac output Portosystemic shunt

Journal

Journal of cardiology cases
ISSN: 1878-5409
Titre abrégé: J Cardiol Cases
Pays: Japan
ID NLM: 101549579

Informations de publication

Date de publication:
Mar 2021
Historique:
received: 01 01 2020
revised: 23 09 2020
accepted: 23 09 2020
entrez: 15 3 2021
pubmed: 16 3 2021
medline: 16 3 2021
Statut: epublish

Résumé

In the late phase after Fontan surgery, organ dysfunction due to high central venous pressure (CVP) is a major clinical problem. We have described the cases of two patients with portosystemic shunts who exhibited hyperammonemia and high cardiac output associated with peripheral vasodilatation after Fontan surgery. A high CVP in these patients may have resulted in the formation of a portosystemic shunt. We performed coil embolization and balloon-occluded retrograde transvenous obliteration for each case. The possibility of a portosystemic shunt as a postoperative complication of Fontan surgery should always be considered. Early detection and therapeutic intervention seem necessary from the viewpoint of stabilizing the Fontan circulation and delaying the progression of liver disorder. <

Identifiants

pubmed: 33717372
doi: 10.1016/j.jccase.2020.10.011
pii: S1878-5409(20)30138-9
pmc: PMC7917403
doi:

Types de publication

Case Reports

Langues

eng

Pagination

103-107

Informations de copyright

© 2020 Japanese College of Cardiology. Published by Elsevier Ltd. All rights reserved.

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Auteurs

Kiyotaka Takefuta (K)

Department of Pediatric Cardiology, Okinawa Prefectural Nanbu Medical Center, Children's Medical Center, Okinawa, Japan.
Department of Pediatrics, International University of Health and Welfare, Narita, Japan.

Hideaki Senzaki (H)

Department of Pediatrics, International University of Health and Welfare, Narita, Japan.

Atsuya Shimabukuro (A)

Department of Pediatric Cardiology, Okinawa Prefectural Nanbu Medical Center, Children's Medical Center, Okinawa, Japan.

Masahiro Nishibata (M)

Department of Pediatric Cardiology, Okinawa Prefectural Nanbu Medical Center, Children's Medical Center, Okinawa, Japan.

Seiichi Sato (S)

Department of Pediatric Cardiology, Okinawa Prefectural Nanbu Medical Center, Children's Medical Center, Okinawa, Japan.

Mami Nakayashiro (M)

Department of Pediatric Cardiology, Okinawa Prefectural Nanbu Medical Center, Children's Medical Center, Okinawa, Japan.

Classifications MeSH