Metastatic renal Ewing's sarcoma in adult woman: Case report and review of the literature.

PNET adult Ewing sarcoma extra-skeletal Ewing sarcoma renal tumor surgical margins

Journal

Open medicine (Warsaw, Poland)
ISSN: 2391-5463
Titre abrégé: Open Med (Wars)
Pays: Poland
ID NLM: 101672167

Informations de publication

Date de publication:
2021
Historique:
received: 17 02 2020
revised: 22 11 2020
accepted: 09 12 2020
entrez: 22 3 2021
pubmed: 23 3 2021
medline: 23 3 2021
Statut: epublish

Résumé

Primary renal extra-skeletal Ewing sarcoma is a rare neoplasm, often metastatic at diagnosis, and with a poor outcome. A multimodal approach is often the treatment of choice in this aggressive neoplasm. We present a case of primary renal extra-skeletal sarcoma in a 45-year-old woman who underwent tumor resection without clear margins. After no response to the first cycle of chemotherapy, we documented an early onset of local recurrence. The patient refused any other treatment and died four months after surgery.

Identifiants

pubmed: 33748424
doi: 10.1515/med-2021-0207
pii: med-2021-0207
pmc: PMC7957192
doi:

Types de publication

Case Reports

Langues

eng

Pagination

397-409

Informations de copyright

© 2021 Giovanni Cochetti et al., published by De Gruyter.

Déclaration de conflit d'intérêts

Conflict of interest: Giovanni Cochetti, and Ettore Mearini serve as Section Editors in Open Medicine, but it hasnt affected the peer-review process, authors do not state any other conflict of interest.

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Auteurs

Giovanni Cochetti (G)

Department of Surgical and Biomedical Sciences, Urology Clinic, University of Perugia, Perugia, Italy.

Alessio Paladini (A)

Department of Surgical and Biomedical Sciences, Urology Clinic, University of Perugia, Perugia, Italy.

Jacopo Adolfo Rossi de Vermandois (JAR)

Department of Surgical and Biomedical Sciences, Urology Clinic, University of Perugia, Perugia, Italy.

Sonia Fatigoni (S)

Department of Surgical and Biomedical Sciences, Medical Oncology, University of Perugia, Perugia, Italy.

Magda Zanelli (M)

Department of Oncology and Advanced Technologies, Pathology Unit, Arcispedale Santa Maria Nuova di Reggio Emilia, AUSL-IRCCS di Reggio Emilia, Reggio Emilia, Italy.

Stefano Ascani (S)

Department of Experimental Medicine, Institute of Pathologic Anatomy, "Santa Maria" Hospital, Terni, Italy.

Ettore Mearini (E)

Department of Surgical and Biomedical Sciences, Urology Clinic, University of Perugia, Perugia, Italy.

Classifications MeSH