Atypical presentations of idiopathic intracranial hypertension.

Idiopathic intracranial hypertension magnetic resonance imaging pseudotumor cerebri

Journal

Taiwan journal of ophthalmology
ISSN: 2211-5072
Titre abrégé: Taiwan J Ophthalmol
Pays: India
ID NLM: 101582127

Informations de publication

Date de publication:
Historique:
received: 29 08 2020
accepted: 11 09 2020
entrez: 26 3 2021
pubmed: 27 3 2021
medline: 27 3 2021
Statut: epublish

Résumé

Idiopathic intracranial hypertension (IIH) is a disorder of unknown etiology that results in isolated raised intracranial pressure. Classic symptoms and signs of IIH include headache, papilledema, diplopia from sixth nerve palsy and divergence insufficiency, and pulsatile tinnitus. Atypical presentations include: (1) highly asymmetric or even unilateral papilledema, and IIH without papilledema; (2) ocular motor disturbances from third nerve palsy, fourth nerve palsy, internuclear ophthalmoplegia, diffuse ophthalmoplegia, and skew deviation; (3) olfactory dysfunction; (4) trigeminal nerve dysfunction; (5) facial nerve dysfunction; (6) hearing loss and vestibular dysfunction; (7) lower cranial nerve dysfunction including deviated uvula, torticollis, and tongue weakness; (8) spontaneous skull base cerebrospinal fluid leak; and (9) seizures. Although atypical findings should raise a red flag and prompt further investigation for an alternative etiology, clinicians should be familiar with these unusual presentations.

Identifiants

pubmed: 33767953
doi: 10.4103/tjo.tjo_69_20
pii: TJO-11-25
pmc: PMC7971435
doi:

Types de publication

Journal Article Review

Langues

eng

Pagination

25-38

Informations de copyright

Copyright: © 2020 Taiwan J Ophthalmol.

Déclaration de conflit d'intérêts

The authors declare that there are no conflicts of interests of this paper.

Références

AJR Am J Roentgenol. 2014 Mar;202(3):608-13
pubmed: 24555598
J Clin Neuroophthalmol. 1985 Sep;5(3):158-63
pubmed: 2934416
Neurology. 1988 Sep;38(9):1461-4
pubmed: 2970600
Surv Ophthalmol. 2020 Jan - Feb;65(1):48-66
pubmed: 31449832
J Child Neurol. 2010 Dec;25(12):1529-34
pubmed: 20921567
Pediatr Neurol. 2002 Mar;26(3):225-7
pubmed: 11955932
J Child Neurol. 1994 Apr;9(2):144-9
pubmed: 8006364
Neurology. 1985 May;35(5):725-8
pubmed: 3990972
J Neuroophthalmol. 2019 Dec;39(4):487-495
pubmed: 30747786
Br J Ophthalmol. 1972 Oct;56(10):776-82
pubmed: 4679659
J Neurol. 2002 Nov;249(11):1601-2
pubmed: 12532926
Headache. 1987 Nov;27(10):573-4
pubmed: 3692820
Neurology. 2013 Sep 24;81(13):1159-65
pubmed: 23966248
Neurol India. 2010 Nov-Dec;58(6):982
pubmed: 21150088
J Neuroophthalmol. 1994 Dec;14(4):196-8
pubmed: 7881522
J Neurol Neurosurg Psychiatry. 1992 Jun;55(6):510-1
pubmed: 1619427
Curr Opin Ophthalmol. 2002 Dec;13(6):371-4
pubmed: 12441839
Neurology. 2001 Jun 12;56(11):1588-90
pubmed: 11402124
Am J Ophthalmol. 1976 Oct;82(4):577-89
pubmed: 61728
J Neuroophthalmol. 2016 Jun;36(2):120-5
pubmed: 26580295
J Neuroophthalmol. 1996 Mar;16(1):49-54
pubmed: 8963421
Neurology. 2016 Jan 26;86(4):341-50
pubmed: 26718577
J Neurol Neurosurg Psychiatry. 1995 Apr;58(4):516
pubmed: 7738578
Otol Neurotol. 2007 Aug;28(5):715-8
pubmed: 17667777
J Neurol Neurosurg Psychiatry. 2018 Oct;89(10):1088-1100
pubmed: 29903905
Radiology. 1997 Jul;204(1):213-9
pubmed: 9205250
Arq Bras Oftalmol. 2019 Jul-Aug;82(4):332-335
pubmed: 31038553
J Neurol Neurosurg Psychiatry. 1990 Apr;53(4):360-1
pubmed: 2341857
J Postgrad Med. 1992 Jul-Sep;38(3):144-5
pubmed: 1303420
J AAPOS. 1998 Feb;2(1):33-8
pubmed: 10532364
Eur J Neurol. 2014 Dec;21(12):1458-64
pubmed: 25070715
Pediatr Neurol. 2002 Mar;26(3):228-30
pubmed: 11955933
PLoS One. 2012;7(4):e35221
pubmed: 22493741
Otol Neurotol. 2009 Jan;30(1):123-4
pubmed: 18277307
Am J Rhinol Allergy. 2021 Jan;35(1):36-43
pubmed: 32551921
Clin Otolaryngol Allied Sci. 1978 May;3(2):183-8
pubmed: 307461
Headache. 2017 Sep;57(8):1195-1205
pubmed: 28752894
J Neuroophthalmol. 2015 Dec;35(4):400-11
pubmed: 26457687
J Clin Neuroophthalmol. 1985 Mar;5(1):41-4
pubmed: 3156888
Eur J Neurol. 2000 Sep;7(5):549-53
pubmed: 11054141
Neurology. 2002 Nov 26;59(10):1492-5
pubmed: 12455560
Pediatr Neurosurg. 2006;42(1):62-4
pubmed: 16357505
J Child Neurol. 2008 May;23(5):580-1
pubmed: 18448574
Eye (Lond). 2019 Mar;33(3):478-485
pubmed: 30356129
Brain Res. 1997 Jan 16;745(1-2):32-6
pubmed: 9037391
Neurol Clin. 2010 Aug;28(3):593-617
pubmed: 20637991
Arch Neurol. 1991 Apr;48(4):392-9
pubmed: 2012512
Headache. 2019 Jun;59(6):848-857
pubmed: 31001819
Ann Otol Rhinol Laryngol. 2015 Dec;124(12):996-1001
pubmed: 26082474
Pediatr Neurol. 1989 Jan-Feb;5(1):5-11
pubmed: 2653341
J Neurol Neurosurg Psychiatry. 1998 Sep;65(3):308-16
pubmed: 9728941
J R Soc Med. 2010 Oct;103(10):412-4
pubmed: 20829324
Pediatr Neurol. 1989 Mar-Apr;5(2):111-3
pubmed: 2712942
J Clin Neuroophthalmol. 1985 Mar;5(1):55-6
pubmed: 3156890
Pediatr Neurol. 2010 Feb;42(2):141-2
pubmed: 20117753
Am J Otol. 1998 Jul;19(4):472-7
pubmed: 9661757
Surv Ophthalmol. 1992 Nov-Dec;37(3):155-66
pubmed: 1475750
Ann Saudi Med. 1997 Mar;17(2):260-1
pubmed: 17377447
Arch Neurol. 1984 Jul;41(7):787-8
pubmed: 6743073
Neurology. 1981 Feb;31(2):182-4
pubmed: 7193301
Am J Ophthalmol. 1999 Feb;127(2):236-7
pubmed: 10030583
Neurol Sci. 2001 Aug;22(4):337
pubmed: 11808860
J Neuroophthalmol. 2020 Aug 19;:
pubmed: 32833859
Ann Otol Rhinol Laryngol. 2020 Aug;129(8):829-832
pubmed: 32390451
J Neurosurg. 1989 Sep;71(3):443-5
pubmed: 2769395
J Assoc Physicians India. 1989 Aug;37(8):533-4
pubmed: 2621191
J Neuroophthalmol. 1996 Mar;16(1):70
pubmed: 8963425
J Neuroophthalmol. 1998 Jun;18(2):121-3
pubmed: 9621269
J Med Case Rep. 2019 Apr 19;13(1):94
pubmed: 30999940
Ann Ophthalmol. 1981 Jan;13(1):53-6
pubmed: 7247159
Invest Ophthalmol Vis Sci. 1998 Jan;39(1):134-42
pubmed: 9430554
Arch Dis Child. 1998 Jan;78(1):89-94
pubmed: 9534686
J Neurosurg. 1982 Dec;57(6):833-6
pubmed: 7143069
Am J Ophthalmol. 2006 Nov;142(5):878-80
pubmed: 17056379
Neurol India. 2010 Sep-Oct;58(5):820-1
pubmed: 21045537
J R Soc Med. 2000 Feb;93(2):80-1
pubmed: 10740577
Arch Ophthalmol. 2000 Sep;118(9):1237-41
pubmed: 10980769
Headache. 2009 Feb;49(2):185-93
pubmed: 19222592
Clin Neurol Neurosurg. 2017 Dec;163:81-83
pubmed: 29078127
Strabismus. 1995;3(2):57-9
pubmed: 21314421
J Neurol Neurosurg Psychiatry. 2003 Apr;74(4):415-8
pubmed: 12640051
Neurol Sci. 2017 May;38(Suppl 1):193-196
pubmed: 28527079
Neurologist. 2018 Sep;23(5):157-159
pubmed: 30169368
Muscle Nerve. 2015 Dec;52(6):927-32
pubmed: 26315943
AJNR Am J Neuroradiol. 2018 Aug;39(8):1468-1472
pubmed: 29903924
Isr Med Assoc J. 2018 Jan;20(1):34-37
pubmed: 29658205
Arch Ophthalmol. 1997 Mar;115(3):423-6
pubmed: 9076222
Ann Neurol. 1978 Dec;4(6):583
pubmed: 742865
Laryngoscope. 1987 Aug;97(S42):1-17
pubmed: 3302575
J Int Adv Otol. 2017 Apr;13(1):100-104
pubmed: 28084997
N Engl J Med. 1977 May 26;296(21):1214-5
pubmed: 854059
Eur J Paediatr Neurol. 2016 Mar;20(2):336-338
pubmed: 26653361
Neurology. 2013 Jul 23;81(4):379-82
pubmed: 23794685
Neurology. 1998 Jun;50(6):1893-6
pubmed: 9633755
Neurology. 1982 Feb;32(2):212-5
pubmed: 7198748
J Neuroophthalmol. 2015 Mar;35(1):31-6
pubmed: 25494197
Neurology. 2002 May 28;58(10):1551-3
pubmed: 12034799
Ann Surg. 1937 Oct;106(4):492-513
pubmed: 17857053
Klin Monbl Augenheilkd. 2008 May;225(5):441-2
pubmed: 18454392
Neuroradiology. 2018 Jan;60(1):51-60
pubmed: 28983769
Arch Neurol. 1982 Jul;39(7):440-2
pubmed: 7103781
Eur J Ophthalmol. 2019 Jul;29(4):NP1-NP4
pubmed: 30280587
Indian J Pediatr. 2005 Dec;72(12):1047-8
pubmed: 16388155
Continuum (Minneap Minn). 2017 Apr;23(2, Selected Topics in Outpatient Neurology):447-466
pubmed: 28375913
Clin Neurol Neurosurg. 2019 Sep;184:105376
pubmed: 31176474
Ann Ophthalmol. 1979 Dec;11(12):1823-7
pubmed: 556136
Front Neurol. 2018 Jun 26;9:503
pubmed: 29997572
Neurology. 2016 Jul 19;87(3):e26-8
pubmed: 27432182
Med Hypotheses. 2008 Nov;71(5):816-7
pubmed: 18584972
Neuroophthalmology. 2016 Oct 5;40(6):292-296
pubmed: 27928421
Saudi Med J. 2007 May;28(5):762-5
pubmed: 17457448
Cephalalgia. 2020 Apr;40(5):429-436
pubmed: 32088969
AMA Arch Neurol Psychiatry. 1951 Dec;66(6):744-51
pubmed: 14877342
Clin Neurophysiol. 2017 Oct;128(10):2048-2049
pubmed: 28863360
Prog Retin Eye Res. 2016 Jan;50:108-44
pubmed: 26453995
Neuroophthalmology. 2018 Jun 26;43(1):3-9
pubmed: 30723518
Curr Opin Ophthalmol. 2019 Nov;30(6):462-466
pubmed: 31567467
JAMA Neurol. 2014 Jun;71(6):693-701
pubmed: 24756302
J Neurol Neurosurg Psychiatry. 1994 Mar;57(3):381
pubmed: 8158193
J Neurol Neurosurg Psychiatry. 2014 Sep;85(9):959-64
pubmed: 24474821
J AAPOS. 2010 Feb;14(1):61-7
pubmed: 20227626
Brain. 2007 Feb;130(Pt 2):514-20
pubmed: 17114796
Can J Ophthalmol. 2015 Oct;50(5):e69-71
pubmed: 26455984
J Headache Pain. 2018 Oct 8;19(1):93
pubmed: 30298346
J Fr Ophtalmol. 2013 Nov;36(9):e173-6
pubmed: 23731791
Laryngoscope. 2019 Nov;129(11):E407-E411
pubmed: 31268557
Laryngoscope. 1990 Nov;100(11):1152-5
pubmed: 2233074
Headache. 1997 May;37(5):286-8
pubmed: 9195767
Laryngoscope. 1990 Jan;100(1):33-6
pubmed: 2293699

Auteurs

Benson S Chen (BS)

Department of Ophthalmology, Emory University School of Medicine, Atlanta, GA, United States.
Department of Neurology, Auckland City Hospital, Auckland, New Zealand.

Nancy J Newman (NJ)

Department of Ophthalmology, Emory University School of Medicine, Atlanta, GA, United States.
Department of Neurology, Emory University School of Medicine, Atlanta, GA, United States.
Department of Neurological Surgery, Emory University School of Medicine, Atlanta, GA, United States.

Valérie Biousse (V)

Department of Ophthalmology, Emory University School of Medicine, Atlanta, GA, United States.
Department of Neurology, Emory University School of Medicine, Atlanta, GA, United States.

Classifications MeSH