TNNI3 and KCNQ1 co-inherited variants in a family with hypertrophic cardiomyopathy and long QT phenotypes: A case report.

ACMG, American College of Medical Genetics and Genomics ECG, electrocardiographic HCM, Hypertrophic cardiomyopathy Hypertrophic cardiomyopathy ICD, Implantable Cardioverter-Defibrillator KCNQ1 LGE, late gadolinium enhancement, late gadolinium enhancement LQTS, long-QT syndrome Long QT syndrome NGS, Next Generation Sequencing Next generation sequencing TNNI3

Journal

Molecular genetics and metabolism reports
ISSN: 2214-4269
Titre abrégé: Mol Genet Metab Rep
Pays: United States
ID NLM: 101624422

Informations de publication

Date de publication:
Jun 2021
Historique:
received: 22 01 2021
revised: 26 02 2021
accepted: 04 03 2021
entrez: 29 3 2021
pubmed: 30 3 2021
medline: 30 3 2021
Statut: epublish

Résumé

QTc prolongation is reported in patients with hypertrophic cardiomyopathy (HCM). However, the causes of the QTc interval increase remain unclear. The main contribution to QTc prolongation in HCM is attributed to the myocardial hypertrophy and related structural damage. In a 24-year-old male proband, affected by HCM and long QTc, we identified by Next Generation Sequencing a pathogenic variant in gene

Identifiants

pubmed: 33777698
doi: 10.1016/j.ymgmr.2021.100743
pii: S2214-4269(21)00037-9
pmc: PMC7985525
doi:

Types de publication

Case Reports

Langues

eng

Pagination

100743

Informations de copyright

© 2021 The Authors.

Déclaration de conflit d'intérêts

None.

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Auteurs

Francesco Cava (F)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.

Ernesto Cristiano (E)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.

Maria Beatrice Musumeci (MB)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.

Camilla Savio (C)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.

Aldo Germani (A)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.
Sant'Andrea University Hospital, Rome 00100, Italy.

Maria Lo Monaco (ML)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.

Simona Petrucci (S)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.
Sant'Andrea University Hospital, Rome 00100, Italy.

Maria Rosaria Torrisi (MR)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.
Sant'Andrea University Hospital, Rome 00100, Italy.

Camillo Autore (C)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.

Speranza Rubattu (S)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.
IRCCS Neuromed, Pozzilli, IS 86077, Italy.

Maria Piane (M)

Department of Clinical and Molecular Medicine, School of Medicine and Psychology, "Sapienza" University of Rome, Rome 00189, Italy.
Sant'Andrea University Hospital, Rome 00100, Italy.

Classifications MeSH