A Nation-Wide, Multi-Center Study on the Quality of Life of ALS Patients in Germany.
ALS treatment
Amyotrophic Lateral Sclerosis (ALS)
Amyotrophic Lateral Sclerosis Assessment Questionnaire 5 (ALSAQ-5)
EuroQol Five Dimension Five Level Scale (EQ-5D-5L)
assistive devices
health-related quality of life (HRQoL)
quality of life (QoL)
symptom-specific treatment
“bulbar-onset” ALS (bALS)
“limb-onset” ALS (lALS)
Journal
Brain sciences
ISSN: 2076-3425
Titre abrégé: Brain Sci
Pays: Switzerland
ID NLM: 101598646
Informations de publication
Date de publication:
14 Mar 2021
14 Mar 2021
Historique:
received:
10
02
2021
revised:
09
03
2021
accepted:
10
03
2021
entrez:
3
4
2021
pubmed:
4
4
2021
medline:
4
4
2021
Statut:
epublish
Résumé
Improving quality of life (QoL) is central to amyotrophic lateral sclerosis (ALS) treatment. This Germany-wide, multicenter cross-sectional study analyses the impact of different symptom-specific treatments and ALS variants on QoL. Health-related QoL (HRQoL) in 325 ALS patients was assessed using the Amyotrophic Lateral Sclerosis Assessment Questionnaire 5 (ALSAQ-5) and EuroQol Five Dimension Five Level Scale (EQ-5D-5L), together with disease severity (captured by the revised ALS Functional Rating Scale (ALSFRS-R)) and the current care and therapies used by our cohort. At inclusion, the mean ALSAQ-5 total score was 56.93 (max. 100, best = 0) with a better QoL associated with a less severe disease status (β = -1.96 per increase of one point in the ALSFRS-R score,
Identifiants
pubmed: 33799476
pii: brainsci11030372
doi: 10.3390/brainsci11030372
pmc: PMC7998410
pii:
doi:
Types de publication
Journal Article
Langues
eng
Subventions
Organisme : German Neuromuscular Society "Deutsche Gesellschaft fuer Muskelkranke" e.V.
ID : Sc23/1
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