Respiratory Manifestations in Systemic Lupus Erythematosus.

airway disease diffuse alveolar hemorrhage infection interstitial lung disease pleurisy shrinking lung syndrome systemic lupus erythematosus

Journal

Pharmaceuticals (Basel, Switzerland)
ISSN: 1424-8247
Titre abrégé: Pharmaceuticals (Basel)
Pays: Switzerland
ID NLM: 101238453

Informations de publication

Date de publication:
18 Mar 2021
Historique:
received: 28 01 2021
revised: 15 03 2021
accepted: 16 03 2021
entrez: 3 4 2021
pubmed: 4 4 2021
medline: 4 4 2021
Statut: epublish

Résumé

Systemic lupus erythematosus (SLE) is a chronic systemic autoimmune disease characterized by a wide spectrum of clinical manifestations. The respiratory system can be involved in up to 50-70% of patients and be the presenting manifestation of the disease in 4-5% of cases. Every part of the respiratory part can be involved, and the severity can vary from mild self-limiting to life threatening forms. Respiratory involvement can be primary (caused by SLE itself) or secondary (e.g., infections or drug toxicity), acute or chronic. The course, treatment and prognosis vary greatly depending on the specific pattern of the disease. This review article aims at providing an overview of respiratory manifestations in SLE along with an update about therapeutic approaches including novel biologic therapies.

Identifiants

pubmed: 33803847
pii: ph14030276
doi: 10.3390/ph14030276
pmc: PMC8003168
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

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Auteurs

Salvatore Di Bartolomeo (S)

Department of Medicine, ASL 1 Avezzano-Sulmona-L'Aquila, 67039 Sulmona, Italy.

Alessia Alunno (A)

Rheumatology Unit, Department of Medicine, University of Perugia, 06123 Perugia, Italy.

Francesco Carubbi (F)

Internal Medicine and Nephrology Unit, Department of Life, Health & Environmental Sciences, University of L'Aquila and Department of Medicine, ASL 1 Avezzano-Sulmona-L'Aquila, 67100 L'Aquila, Italy.

Classifications MeSH