Hirayama-like disease in the thoracic spine.
Dorsal ligamentous laxity
Hirayama disease
Spinal vascular malformation
Spine MRA
Spine MRI
Thoracic spine
Journal
Radiology case reports
ISSN: 1930-0433
Titre abrégé: Radiol Case Rep
Pays: Netherlands
ID NLM: 101467888
Informations de publication
Date de publication:
May 2021
May 2021
Historique:
received:
13
02
2021
accepted:
20
02
2021
entrez:
5
4
2021
pubmed:
6
4
2021
medline:
6
4
2021
Statut:
epublish
Résumé
Hirayama disease is a cervical flexion myelopathy that typically causes upper extremity weakness in young male patients. We present two male patients (age 15 and 29) with MRI findings of thoracic ligamentous laxity similar in appearance to Hirayama disease. However, patients presented with atypical symptoms, specifically back pain and paresthesia of the upper and/or lower extremities, likely correlating to the abnormal thoracic spinal levels involved. Flexion/extension MRI sequences demonstrated the forward displacement of the dorsal dura and compression the thoracic cord with prominence of the posterior epidural space and venous plexus. Follow-up MRAs were negative for a spinal vascular malformation. Patients were managed conservatively with no surgical intervention. Clinical history, thoracic MRI, and follow-up flexion and angiographic imaging sequences may help confirm a diagnosis of Hirayama-like thoracic ligamentous laxity.
Identifiants
pubmed: 33815645
doi: 10.1016/j.radcr.2021.02.039
pii: S1930-0433(21)00103-5
pmc: PMC8010572
doi:
Types de publication
Case Reports
Langues
eng
Pagination
1216-1219Informations de copyright
© 2021 The Authors. Published by Elsevier Inc. on behalf of University of Washington.
Références
AJNR Am J Neuroradiol. 2018 May;39(5):974-980
pubmed: 29545250
World Neurosurg. 2020 Oct;142:325-327
pubmed: 32673810
Radiology. 2004 Apr;231(1):39-44
pubmed: 15068939
Neurology. 2004 Apr 27;62(8):1426-8
pubmed: 15111690
AJNR Am J Neuroradiol. 2013 Feb;34(2):451-6
pubmed: 22878010
Radiol Case Rep. 2020 Jul 22;15(9):1701-1704
pubmed: 32742532
Case Rep Neurol. 2019 Mar 21;11(1):106-111
pubmed: 31011327
J Neuroimaging. 2019 Nov;29(6):673-688
pubmed: 31529762
J Med Case Rep. 2020 Aug 21;14(1):133
pubmed: 32819426
Eur Spine J. 2002 Jun;11(3):276-85
pubmed: 12107798