Severe and progressive platythorax disproportionate to lung fibrosis: A rare variant of idiopathic pleuroparenchymal fibroelastosis.
Emaciation
Flat chest index
Platythorax
Pleuroparenchymal fibroelastosis
Journal
Respiratory medicine case reports
ISSN: 2213-0071
Titre abrégé: Respir Med Case Rep
Pays: England
ID NLM: 101604463
Informations de publication
Date de publication:
2021
2021
Historique:
received:
01
03
2021
revised:
12
03
2021
accepted:
16
03
2021
entrez:
5
4
2021
pubmed:
6
4
2021
medline:
6
4
2021
Statut:
epublish
Résumé
A 57-year-old man was referred to our department because of progressive shortness of breath and emaciation. He had experienced pneumothorax three times in the past five years. The patient radiologically showed mild upper-lobe predominant airspace consolidation and severe platythorax and was clinically diagnosed with idiopathic pleuroparenchymal fibroelastosis (PPFE). Although the wedge-shaped shadows in the bilateral lung apexes did not significantly progress, his platythorax gradually worsened during the clinical course. He ultimately died of chronic respiratory failure 1.2 years after the diagnosis. This case demonstrates a rare variant of idiopathic PPFE with progressive platythorax disproportionate to the extent of upper-lobe fibroelastosis.
Identifiants
pubmed: 33816104
doi: 10.1016/j.rmcr.2021.101395
pii: S2213-0071(21)00057-5
pmc: PMC8008244
doi:
Types de publication
Case Reports
Langues
eng
Pagination
101395Informations de copyright
© 2021 The Author(s).
Déclaration de conflit d'intérêts
The authors have no conflicts of interest directly relevant to the content of this article.
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