Atrioventricular Discordance with Double-Outlet Right Ventricle in Mirror Imagery and Levocardia: A Very Rare Case Report.

Atrioventricular discordance double-outlet right ventricle levocardia mirror-imagery

Journal

Journal of cardiovascular echography
ISSN: 2211-4122
Titre abrégé: J Cardiovasc Echogr
Pays: India
ID NLM: 101562228

Informations de publication

Date de publication:
Historique:
received: 20 06 2020
revised: 15 10 2020
accepted: 18 10 2020
entrez: 8 4 2021
pubmed: 9 4 2021
medline: 9 4 2021
Statut: ppublish

Résumé

A newborn without prenatal diagnosis, with bronchial and abdominal situs inversus in levocardia, was referred to our hospital for accurate evaluation; echocardiography showed venoatrial connections in mirror-image arrangement, atrioventricular (AV) discordance, and double-outlet right ventricle (DORV). Additional cardiac malformations were double upper caval district, atrial communication, subpulmonary interventricular communication, and moderate subvalvular and valvular pulmonary stenosis. Few days after birth, the patient presented low oxygen saturation and the heart team decided for a palliative surgery. We describe a very rare case in a newborn with bronchial-abdominal mirror imagery, AV discordance, and DORV in levocardia.

Identifiants

pubmed: 33828947
doi: 10.4103/jcecho.jcecho_65_20
pii: JCE-30-227
pmc: PMC8021085
doi:

Types de publication

Case Reports

Langues

eng

Pagination

227-230

Informations de copyright

Copyright: © 2021 Journal of Cardiovascular Echography.

Déclaration de conflit d'intérêts

There are no conflicts of interest.

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Auteurs

Silvia Farruggio (S)

Mediterranean Pediatric Cardiology Center "Bambino Gesù", San Vincenzo Hospital, Taormina, ME, Italy.

Salvatore Agati (S)

Mediterranean Pediatric Cardiology Center "Bambino Gesù", San Vincenzo Hospital, Taormina, ME, Italy.

Davide Calvaruso (D)

Mediterranean Pediatric Cardiology Center "Bambino Gesù", San Vincenzo Hospital, Taormina, ME, Italy.

Corrado Di Mambro (CD)

Mediterranean Pediatric Cardiology Center "Bambino Gesù", San Vincenzo Hospital, Taormina, ME, Italy.

Elio Caruso (E)

Mediterranean Pediatric Cardiology Center "Bambino Gesù", San Vincenzo Hospital, Taormina, ME, Italy.

Classifications MeSH