Use of Next-Generation Sequencing for the Molecular Diagnosis of 1,102 Patients With a Autosomal Optic Neuropathy.

inherited optic neuropathies mitochondrial disorders molecular diagnosis next generation sequencing retinal ganglia cells

Journal

Frontiers in neurology
ISSN: 1664-2295
Titre abrégé: Front Neurol
Pays: Switzerland
ID NLM: 101546899

Informations de publication

Date de publication:
2021
Historique:
received: 04 09 2020
accepted: 01 02 2021
entrez: 12 4 2021
pubmed: 13 4 2021
medline: 13 4 2021
Statut: epublish

Résumé

Advances in next-generation sequencing (NGS) facilitate the diagnosis of genetic disorders. To evaluate its use for the molecular diagnosis of inherited optic neuropathy (ION), a blinding disease caused by the degeneration of retinal ganglion cells, we performed genetic analysis using targeted NGS of 22 already known and candidate genes in a cohort of 1,102 affected individuals. The panel design, library preparation, and sequencing reactions were performed using the Ion AmpliSeq technology. Pathogenic variants were detected in 16 genes in 245 patients (22%), including 186 (17%) and 59 (5%) dominant and recessive cases, respectively. Results confirmed that

Identifiants

pubmed: 33841295
doi: 10.3389/fneur.2021.602979
pmc: PMC8027346
doi:

Types de publication

Journal Article

Langues

eng

Pagination

602979

Informations de copyright

Copyright © 2021 Charif, Bris, Goudenège, Desquiret-Dumas, Colin, Ziegler, Procaccio, Reynier, Bonneau, Lenaers and Amati-Bonneau.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Majida Charif (M)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Genetics and Immuno-Cell Therapy Team, Mohammed First University, Oujda, Morocco.

Céline Bris (C)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

David Goudenège (D)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Valérie Desquiret-Dumas (V)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Estelle Colin (E)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Alban Ziegler (A)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Vincent Procaccio (V)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Pascal Reynier (P)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Dominique Bonneau (D)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Guy Lenaers (G)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.

Patrizia Amati-Bonneau (P)

University Angers, MitoLab team, UMR CNRS 6015-INSERM U1083, Unité MitoVasc, SFR ICAT, Angers, France.
Departments of Biochemistry and Genetics, University Hospital Angers, Angers, France.

Classifications MeSH