Management of respiratory complications and rehabilitation in individuals with muscular dystrophies: 1st Consensus Conference report from UILDM - Italian Muscular Dystrophy Association (Milan, January 25-26, 2019).
arterial blood gases
cough efficacy
cough machine
invasive ventilation
mechanical ventilation
muscular dystrophy
non-invasive ventilation
polygraphy
respiratory failure
spirometry
tracheostomy
Journal
Acta myologica : myopathies and cardiomyopathies : official journal of the Mediterranean Society of Myology
ISSN: 2532-1900
Titre abrégé: Acta Myol
Pays: Italy
ID NLM: 9811169
Informations de publication
Date de publication:
Mar 2021
Mar 2021
Historique:
received:
16
03
2021
accepted:
16
03
2021
entrez:
19
4
2021
pubmed:
20
4
2021
medline:
5
11
2021
Statut:
epublish
Résumé
Respiratory complications are common in the patient with muscular dystrophy. The periodic clinical and instrumental respiratory evaluation is extremely important. Despite the presence in the literature of updated guidelines, patient associations often report lack of knowledge of these pathologies, particularly in peripheral hospitals. The purpose of this work, inspired by the Italian Muscular Dystrophy Association (UILDM) is to improve management of respiratory problems necessary for the management of these patients complex. To this end, the main items that the specialist can meet in the follow-up of these pathologies have been analyzed and discussed, among which the respiratory basal evaluation, the criteria of adaptation to non-invasive ventilation, management of bronchial secretions, situations of respiratory emergency, indications for tracheostomy and the subject of advance directives of treatment (DAT).
Identifiants
pubmed: 33870094
doi: 10.36185/2532-1900-045
pmc: PMC8033426
doi:
Types de publication
Consensus Development Conference
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
8-42Investigateurs
Alessio Mattei
(A)
Grazia Crescimanno
(G)
Elisabetta Roma
(E)
Antonello Nicolini
(A)
Anna Mandelli
(A)
Alessia Fabiano
(A)
Mirco Lusuardi
(M)
Antonella Pini
(A)
Maurizio Grandi
(M)
Federico Sciarra
(F)
Emiliana Meleo
(E)
Claudia Profazio
(C)
Vilma Donizetti
(V)
Marino Iatomasi
(M)
Informations de copyright
©2021 Gaetano Conte Academy - Mediterranean Society of Myology, Naples, Italy.
Déclaration de conflit d'intérêts
Conflict of interest The Authors declare no conflict of interest
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