[Uniform classification of the pachychoroid spectrum disorders].
Einheitliche Klassifikation des pachychorioidalen Krankheitsspektrums.
Central serous chorioretinopathy
Focal choroidal excavation
Pachychoroid neovasculopathy
Pachychoroid pigment epitheliopathy
Peripapillary pachychoroid syndrome
Journal
Der Ophthalmologe : Zeitschrift der Deutschen Ophthalmologischen Gesellschaft
ISSN: 1433-0423
Titre abrégé: Ophthalmologe
Pays: Germany
ID NLM: 9206148
Informations de publication
Date de publication:
Aug 2021
Aug 2021
Historique:
accepted:
19
03
2021
pubmed:
27
4
2021
medline:
10
8
2021
entrez:
26
4
2021
Statut:
ppublish
Résumé
Pachychoroid spectrum disorders are characterized by a thickening of the choroid. The spectrum includes pachychoroid pigment epitheliopathy (PPE), central serous chorioretinopathy (CCS), pachychoroid neovasculopathy (PNV), polypoidal choroidal vasculopathy (PCV)/aneurysmal type 1 choroidal neovascularization (ACNV-1), focal choroidal excavation (FCE) and peripapillary pachychoroid syndrome (PPS). If the choroid is thickened and there is a pathological alteration in the retinal pigment epithelium, the diagnosis is PPE; if the thickened choroid is accompanied by subretinal fluid, the diagnosis is CCS; if choroidal neovascularization is present, the diagnosis is PNV; if accompanied by aneurysms, the diagnosis is ACNV‑1. The PPE, CCS, PNV and ACNV‑1 were formerly regarded as independent disease entities but can be classified into four forms of a single disease family, pachychoroid macular disease. Die pachychorioidalen Erkrankungen sind alle durch eine Verdickung der Aderhaut gekennzeichnet. Die Gruppe umfasst die folgenden Krankheitsgruppen: pachychorioidale Pigmentepitheliopathie (PPE), Chorioretinopathia centralis serosa (CCS), pachychorioidale Neovaskulopathie (PNV), polypoidale chorioidale Vaskulopathie (PCV)/aneurysmatische chorioidale Neovaskularisation Typ 1 (ACNV‑1), fokale chorioidale Exkavation (FCE) und peripapilläres pachychorioidales Syndrom (PPS). Wenn bei verdickter Aderhaut zusätzlich eine Veränderung des retinalen Pigmentepithels vorliegt, lautet die Diagnose PPE; wenn die verdickte Aderhaut von subretinaler Flüssigkeit begleitet ist, lautet die Diagnose CCS; wenn eine chorioidale Neovaskularisation vorliegt, lautet die Diagnose PNV; wenn sie von Aneurysmen begleitet ist, lautet die Diagnose ACNV‑1. PPE, CCS, PNV und ACNV‑1 wurden als unabhängige Krankheitsentitäten angesehen, lassen sich aber als 4 Formen einer einzigen Krankheitsfamilie, der „pachychorioidalen Makulaerkrankung“, klassifizieren.
Autres résumés
Type: Publisher
(ger)
Die pachychorioidalen Erkrankungen sind alle durch eine Verdickung der Aderhaut gekennzeichnet. Die Gruppe umfasst die folgenden Krankheitsgruppen: pachychorioidale Pigmentepitheliopathie (PPE), Chorioretinopathia centralis serosa (CCS), pachychorioidale Neovaskulopathie (PNV), polypoidale chorioidale Vaskulopathie (PCV)/aneurysmatische chorioidale Neovaskularisation Typ 1 (ACNV‑1), fokale chorioidale Exkavation (FCE) und peripapilläres pachychorioidales Syndrom (PPS). Wenn bei verdickter Aderhaut zusätzlich eine Veränderung des retinalen Pigmentepithels vorliegt, lautet die Diagnose PPE; wenn die verdickte Aderhaut von subretinaler Flüssigkeit begleitet ist, lautet die Diagnose CCS; wenn eine chorioidale Neovaskularisation vorliegt, lautet die Diagnose PNV; wenn sie von Aneurysmen begleitet ist, lautet die Diagnose ACNV‑1. PPE, CCS, PNV und ACNV‑1 wurden als unabhängige Krankheitsentitäten angesehen, lassen sich aber als 4 Formen einer einzigen Krankheitsfamilie, der „pachychorioidalen Makulaerkrankung“, klassifizieren.
Identifiants
pubmed: 33900429
doi: 10.1007/s00347-021-01379-4
pii: 10.1007/s00347-021-01379-4
doi:
Types de publication
Journal Article
Langues
ger
Sous-ensembles de citation
IM
Pagination
865-878Commentaires et corrections
Type : CommentIn
Informations de copyright
© 2021. Springer Medizin Verlag GmbH, ein Teil von Springer Nature.
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