Loss of PKD1 and PKD2 share common effects on intracellular Ca

ADPKD Anoctamin 1 Ca(2+) activated Cl(−) channel Pkd1 Pkd2 Renal cysts TMEM16A

Journal

Cell calcium
ISSN: 1532-1991
Titre abrégé: Cell Calcium
Pays: Netherlands
ID NLM: 8006226

Informations de publication

Date de publication:
24 Apr 2021
Historique:
received: 30 11 2020
revised: 17 04 2021
accepted: 18 04 2021
pubmed: 30 4 2021
medline: 30 4 2021
entrez: 29 4 2021
Statut: aheadofprint

Résumé

In polycystic kidney disease (PKD) multiple bilateral renal cysts gradually enlarge causing a decline in renal function. Transepithelial chloride secretion through cystic fibrosis transmembrane conductance regulator (CFTR) and TMEM16A (anoctamin 1) drive cyst enlargement. We demonstrated recently that a loss of PKD1 increases expression and function of TMEM16A in murine kidneys and in mouse M1 collecting duct cells. The data demonstrated that TMEM16A contributes essentially to cyst growth by upregulating intracellular Ca

Identifiants

pubmed: 33915319
pii: S0143-4160(21)00067-1
doi: 10.1016/j.ceca.2021.102413
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

102413

Informations de copyright

Copyright © 2021 Elsevier Ltd. All rights reserved.

Auteurs

Ines Cabrita (I)

Institut für Physiologie, Universität Regensburg, Universitätsstraße 31, D-93053 Regensburg, Germany.

Khaoula Talbi (K)

Institut für Physiologie, Universität Regensburg, Universitätsstraße 31, D-93053 Regensburg, Germany.

Karl Kunzelmann (K)

Institut für Physiologie, Universität Regensburg, Universitätsstraße 31, D-93053 Regensburg, Germany. Electronic address: karl.kunzelmann@ur.de.

Rainer Schreiber (R)

Institut für Physiologie, Universität Regensburg, Universitätsstraße 31, D-93053 Regensburg, Germany.

Classifications MeSH