Extra-axial, dural-based atypical teratoid/rhabdoid tumor.
ATRT
Atypical
Dural
Embryonal
Extra axial
Pediatric
Rhabdoid
Teratoid
Journal
Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
ISSN: 1433-0350
Titre abrégé: Childs Nerv Syst
Pays: Germany
ID NLM: 8503227
Informations de publication
Date de publication:
03 2022
03 2022
Historique:
received:
20
01
2021
accepted:
28
04
2021
pubmed:
5
5
2021
medline:
5
4
2022
entrez:
4
5
2021
Statut:
ppublish
Résumé
Atypical teratoid/rhabdoid tumors (ATRTs) are malignant central nervous system tumors that affect early childhood (< 3 years), and mostly located in the infratentorial space. Owing to an infrequent occurrence, their radiological features have not been completely defined. Nevertheless, these are characteristically intra-axial except for few instances in the cerebellopontine angle region. We describe a case of a 10-year-old boy who harbored an extra-axial, dural-based ATRT in the right parietal region. The lesion was totally excised followed by adjuvant chemo-radiotherapy. At 10-month follow-up, he was well with no recurrence. The report intends to highlight an atypical imaging presentation of ATRT in an older child, and adds to the radiological spectrum. This uncommon pathology should be borne in mind, even in a supratentorial dural-based location.
Identifiants
pubmed: 33944990
doi: 10.1007/s00381-021-05196-7
pii: 10.1007/s00381-021-05196-7
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
655-658Informations de copyright
© 2021. The Author(s), under exclusive licence to Springer-Verlag GmbH Germany, part of Springer Nature.
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