Spontaneous cervical swelling syndrome as a rare cause of neck edema: case series and literature review.


Journal

Oxford medical case reports
ISSN: 2053-8855
Titre abrégé: Oxf Med Case Reports
Pays: England
ID NLM: 101642070

Informations de publication

Date de publication:
May 2021
Historique:
received: 23 11 2020
revised: 08 03 2021
accepted: 19 03 2021
entrez: 31 5 2021
pubmed: 1 6 2021
medline: 1 6 2021
Statut: epublish

Résumé

Spontaneous cervical swelling syndrome (SCSS) is a rare disorder characterized by unprovoked, self-limiting and often unilateral cervical edema. SCSS is a recurrent disorder that predominantly affects adult women and is not associated with laboratory abnormalities. We report on eight female patients with a mean age of 56 (38-82) years at the time of the first presentation. The episodes were characterized by an acute onset in all patients and had a mean duration of 3.8 (1-7) days. Biochemical analysis did not reveal any related abnormalities. Imaging of the neck and chest demonstrated diffuse edema in the supraclavicular fossa and left infrahyoid region in all patients. At the time of the acute event, lymphatic scintigraphy revealed tracer accumulation in the left supraclavicular region in three patients and could not demonstrate any abnormalities in the in-between episodes in two patients.

Identifiants

pubmed: 34055365
doi: 10.1093/omcr/omab029
pii: omab029
pmc: PMC8143671
doi:

Types de publication

Case Reports

Langues

eng

Pagination

omab029

Informations de copyright

© The Author(s) 2021. Published by Oxford University Press. All rights reserved. For Permissions, please email: journals.permissions@oup.com.

Références

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pubmed: 21705477
Auris Nasus Larynx. 2010 Aug;37(4):535-7
pubmed: 20031353
Head Neck. 1992 Jan-Feb;14(1):1-7
pubmed: 1624288

Auteurs

Albrecht Betrains (A)

Department of General Internal Medicine, University Hospitals Leuven, Leuven, Belgium.
Laboratory of Clinical Infectious and Inflammatory disease, Department of Microbiology, Immunology and Transplant medicine, University Hospitals Leuven, Leuven, Belgium.

Robert Hermans (R)

Department of Radiology, University Hospitals Leuven, Leuven, Belgium.
Department of Imaging and Pathology, University Hospitals Leuven, Leuven, Belgium.

Olivier Gheysens (O)

Department of Imaging and Pathology, University Hospitals Leuven, Leuven, Belgium.
Nuclear medicine and Molecular Imaging, University Hospitals Leuven, Leuven, Belgium.

Vincent Vander Poorten (VV)

Department of Otorhinolaryngology, University Hospitals Leuven, Leuven, Belgium.
Department of Oncology, University Hospitals Leuven, Leuven, Belgium.

Willy E Peetermans (WE)

Laboratory of Clinical Infectious and Inflammatory disease, Department of Microbiology, Immunology and Transplant medicine, University Hospitals Leuven, Leuven, Belgium.

Steven Vanderschueren (S)

Laboratory of Clinical Infectious and Inflammatory disease, Department of Microbiology, Immunology and Transplant medicine, University Hospitals Leuven, Leuven, Belgium.

Classifications MeSH