Persistent Hypoglycemia with Polycystic Kidneys: A Rare Combination - A Case Report.

Hyperinsulinemic hypoglycemia PMM2 gene mutation Polycystic kidney disease

Journal

Biomedicine hub
ISSN: 2296-6870
Titre abrégé: Biomed Hub
Pays: Switzerland
ID NLM: 101692630

Informations de publication

Date de publication:
Historique:
received: 16 06 2020
accepted: 07 09 2020
entrez: 31 5 2021
pubmed: 1 6 2021
medline: 1 6 2021
Statut: epublish

Résumé

We present the case of an infant referred to our NICU born at 39 weeks' gestation with persistent hypoglycemia with elevated insulin levels (HI) requiring diazoxide to maintain normoglycemia. Additionally, polycystic kidney disease (PKD) was detected by ultrasound. Molecular genetic testing revealed pathogenic variants in the

Identifiants

pubmed: 34055813
doi: 10.1159/000511389
pii: bmh-0005-0032
pmc: PMC8136312
doi:

Types de publication

Case Reports

Langues

eng

Pagination

32-37

Subventions

Organisme : NIDDK NIH HHS
ID : T32 DK007695
Pays : United States

Informations de copyright

Copyright © 2020 by S. Karger AG, Basel.

Déclaration de conflit d'intérêts

The authors have no conflicts of interest − personal, professional, or financial − to disclose.

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Auteurs

Priya Prasher (P)

Department of Pediatrics, Marshall University, Joan C Edwards School of Medicine, Huntington, West Virginia, USA.

Katherine Redmond (K)

Department of Pediatrics, Marshall University, Joan C Edwards School of Medicine, Huntington, West Virginia, USA.

Hillarey Stone (H)

Division of Nephrology and Hypertension, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.

James Bailes (J)

Division of Endocrinology, Hoops Family Children's Hospital at Cabell Huntington Hospital, Huntington, West Virginia, USA.

Edward Nehus (E)

Division of Nephrology and Hypertension, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.

Deborah Preston (D)

Department of Pediatrics, Marshall University, Joan C Edwards School of Medicine, Huntington, West Virginia, USA.

Joseph Werthammer (J)

Department of Pediatrics, Marshall University, Joan C Edwards School of Medicine, Huntington, West Virginia, USA.
Department of Pediatrics, Marshall University, Joan C Edwards School of Medicine, Huntington, West Virginia, USA.
Division of Nephrology and Hypertension, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.
Division of Endocrinology, Hoops Family Children's Hospital at Cabell Huntington Hospital, Huntington, West Virginia, USA.

Classifications MeSH