Neurofibromin Deficiency and Extracellular Matrix Cooperate to Increase Transforming Potential through FAK-Dependent Signaling.
FAK
MEK inhibitor
extracellular matrix
neurofibromatosis type 1
tumor therapy
Journal
Cancers
ISSN: 2072-6694
Titre abrégé: Cancers (Basel)
Pays: Switzerland
ID NLM: 101526829
Informations de publication
Date de publication:
12 May 2021
12 May 2021
Historique:
received:
27
02
2021
revised:
06
05
2021
accepted:
07
05
2021
entrez:
2
6
2021
pubmed:
3
6
2021
medline:
3
6
2021
Statut:
epublish
Résumé
Plexiform neurofibromas (Pnfs) are benign peripheral nerve sheath tumors that are major features of the human genetic syndrome, neurofibromatosis type 1 (NF1). Pnfs are derived from Schwann cells (SCs) undergoing loss of heterozygosity (LOH) at the
Identifiants
pubmed: 34066061
pii: cancers13102329
doi: 10.3390/cancers13102329
pmc: PMC8150846
pii:
doi:
Types de publication
Journal Article
Langues
eng
Subventions
Organisme : Neurofibromatosis Therapy Acceleration Program
ID : 10 80028823
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