Poorly Differentiated Neuroendocrine Larynx Carcinoma: Clinical Features and miRNAs Signature-A New Goal for Early Diagnosis and Therapy?

carcinoma larynx miRNA neuroendocrine poorly differentiated squamous

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
08 May 2021
Historique:
received: 28 03 2021
revised: 27 04 2021
accepted: 29 04 2021
entrez: 2 6 2021
pubmed: 3 6 2021
medline: 3 6 2021
Statut: epublish

Résumé

Laryngeal neuroendocrine carcinomas (LNECs) are rare and highly heterogeneous malignancies presenting a wide range of pathological and clinical manifestations. Herein, we retrospectively characterize ten patients diagnosticated with LNEC, five of which were defined as well-moderately differentiated neuroendocrine carcinomas, and five that were defined as poorly differentiated neuroendocrine carcinomas, according to the latest WHO classification. Clinical features were analyzed and compared between the two subgroups together with a microRNA study which evidenced a peculiar signature likely related to poorly differentiated larynx neuroendocrine carcinomas. These findings may offer new useful insights for clinicians to improve diagnosis efficiency, therapy response, and patients' outcome for this aggressive neoplasm.

Identifiants

pubmed: 34066893
pii: jcm10092019
doi: 10.3390/jcm10092019
pmc: PMC8125889
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : POR Campania FESR 2014/2020
ID : project SENSORMIRCIRCOLAR and by FSN 2014-2015-2016 Linea 5/11.

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Auteurs

Filippo Ricciardiello (F)

U.O.C. Otolaryngology, AORN "Antonio Cardarelli", 80131 Napoli, Italy.

Michela Falco (M)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", 80138 Naples, Italy.

Giuseppe Tortoriello (G)

U.O.C. Otolaryngology, ASL-NA1 Ospedale del Mare, 80147 Naples, Italy.

Ferdinando Riccardi (F)

U.O.C. Oncology, AORN "Antonio Cardarelli", 80131 Naples, Italy.

Raul Pellini (R)

U.O.C. Otolaryngology-Head and Neck Surgery, IRCCS Regina Elena National Cancer Institute, 00161 Rome, Italy.

Brigida Iorio (B)

U.O.C. Otolaryngology, San Paolo Hospital, ASL Napoli 1, 80145 Naples, Italy.

Giuseppe Russo (G)

U.O.C. General Direction, AORN "Antonio Cardarelli", 80131 Naples, Italy.

Giuseppe Longo (G)

U.O.C. Healthcare Direction, AORN "Antonio Cardarelli", 80131 Naples, Italy.

Ciro Coppola (C)

U.O.C. General Direction, AORN "Antonio Cardarelli", 80131 Naples, Italy.

Takashi Takeuchi (T)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", 80138 Naples, Italy.
Molecular Diagnostics Division, Wakunaga Pharmaceutical Co., Ltd., Hiroshima 739-1195, Japan.

Anna Grimaldi (A)

U.P. Diagnostics Cytometric and Mutational, Vanvitelli Hospital, 80138 Naples, Italy.

Marianna Abate (M)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", 80138 Naples, Italy.

Marianna Scrima (M)

Laboratory of Molecular and Precision Oncology, Biogem Institute of Molecular Biology and Genetics, 83031 Ariano Irpino, Italy.

Alessia Maria Cossu (AM)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", 80138 Naples, Italy.
Laboratory of Molecular and Precision Oncology, Biogem Institute of Molecular Biology and Genetics, 83031 Ariano Irpino, Italy.

Raffaele Addeo (R)

U.O.C Oncology, Day Hospital, San Giovanni di Dio Hospital, ASL Naples 2 Nord, 80020 Frattamaggiore, Italy.

Alessandro Ottaiano (A)

S.S.D. Innovative Therapies for Abdominal Metastases, Istituto Nazionale Tumori, IRCCS Fondazione G. Pascale, 80131 Naples, Italy.

Alfonso Scarpa (A)

U.O.C Medicine, Surgery and Dentistry, University of Salerno, 84081 Baronissi, Italy.

Amedeo Boscaino (A)

U.O.C Pathologic Anatomy, AORN "Antonio Cardarelli", 80131 Naples, Italy.

Giovanni Motta (G)

U.O.C. Otolaryngology, AORN "Antonio Cardarelli", 80131 Napoli, Italy.

Michele Caraglia (M)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", 80138 Naples, Italy.
Laboratory of Molecular and Precision Oncology, Biogem Institute of Molecular Biology and Genetics, 83031 Ariano Irpino, Italy.

Marco Bocchetti (M)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", 80138 Naples, Italy.
Laboratory of Molecular and Precision Oncology, Biogem Institute of Molecular Biology and Genetics, 83031 Ariano Irpino, Italy.

Gabriella Misso (G)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", 80138 Naples, Italy.

Classifications MeSH