HEV-Associated Neuralgic Amyotrophy: A Multicentric Case Series.

HEV Hepatitis E NA neuralgic amyotrophy

Journal

Pathogens (Basel, Switzerland)
ISSN: 2076-0817
Titre abrégé: Pathogens
Pays: Switzerland
ID NLM: 101596317

Informations de publication

Date de publication:
30 05 2021
Historique:
received: 20 04 2021
revised: 22 05 2021
accepted: 25 05 2021
entrez: 2 6 2021
pubmed: 3 6 2021
medline: 3 6 2021
Statut: epublish

Résumé

Neuralgic amyotrophy (NA) has been described as a possible extrahepatic manifestation of hepatitis E virus (HEV) infection. Usually, HEV-associated NA occurs bilaterally. The clinical characteristics determining the course of HEV-associated NA have still not been defined. In this retrospective multicentric case series, 16 patients with HEV-associated NA were studied and compared to 176 HEV patients without NA in terms of their age, sex, and ALT levels. Neither gender distribution (75% vs. 67% male) nor age (47 vs. 48 years median) differed significantly between the NA patients and controls. Eight NA patients (50%) presented with bilateral involvement-seven of these had right-side dominance and one had left-side dominance. Thirteen cases (81%) were hospitalized. Eight of these patients stayed in hospital for five to seven days, and five patients stayed for up to two weeks. The time from the onset of NA to the HEV diagnosis, as well as the diagnostic and therapeutic proceedings, showed a large variability. In total, 13 (81%) patients received treatment: 1/13 (8%) received intravenous immunoglobulins, 8/13 (62%) received glucocorticoids, 3/13 (23%) received ribavirin, and 6/13 (46%) received pregabalin/gabapentin. Patients with ages above the median (47 years) were more likely to be treated ( HEV-associated NA causes a relevant morbidity. In our case series neither the type of treatment nor the time of initiation of therapy had a significant effect on the duration of hospitalization or the course of the disease. The clinical presentation, the common diagnostic and therapeutic procedures, and the patients' characteristics showed large variability, demonstrating the necessity of standardized protocols for this rare but relevant disease.

Sections du résumé

BACKGROUND
Neuralgic amyotrophy (NA) has been described as a possible extrahepatic manifestation of hepatitis E virus (HEV) infection. Usually, HEV-associated NA occurs bilaterally. The clinical characteristics determining the course of HEV-associated NA have still not been defined.
METHODS
In this retrospective multicentric case series, 16 patients with HEV-associated NA were studied and compared to 176 HEV patients without NA in terms of their age, sex, and ALT levels.
RESULTS
Neither gender distribution (75% vs. 67% male) nor age (47 vs. 48 years median) differed significantly between the NA patients and controls. Eight NA patients (50%) presented with bilateral involvement-seven of these had right-side dominance and one had left-side dominance. Thirteen cases (81%) were hospitalized. Eight of these patients stayed in hospital for five to seven days, and five patients stayed for up to two weeks. The time from the onset of NA to the HEV diagnosis, as well as the diagnostic and therapeutic proceedings, showed a large variability. In total, 13 (81%) patients received treatment: 1/13 (8%) received intravenous immunoglobulins, 8/13 (62%) received glucocorticoids, 3/13 (23%) received ribavirin, and 6/13 (46%) received pregabalin/gabapentin. Patients with ages above the median (47 years) were more likely to be treated (
CONCLUSION
HEV-associated NA causes a relevant morbidity. In our case series neither the type of treatment nor the time of initiation of therapy had a significant effect on the duration of hospitalization or the course of the disease. The clinical presentation, the common diagnostic and therapeutic procedures, and the patients' characteristics showed large variability, demonstrating the necessity of standardized protocols for this rare but relevant disease.

Identifiants

pubmed: 34070707
pii: pathogens10060672
doi: 10.3390/pathogens10060672
pmc: PMC8230081
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Deutsches Zentrum für Infektionsforschung
ID : DZIF TI 07.001
Organisme : Else Kröner-Fresenius-Stiftung
ID : 2019: EKFS10

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Auteurs

Johannes H Bannasch (JH)

Institute of Medical Microbiology, Virology and Hygiene, University Medical Centre Hamburg-Eppendorf, 20251 Hamburg, Germany
Department of Medicine, University Medical Centre Hamburg-Eppendorf, 20251 Hamburg, Germany
German Center for Infection Research (DZIF), Hamburg-Lübeck-Borstel and Heidelberg Partner Sites, 20359 Hamburg, Germany

Benjamin Berger (B)

Clinic of Neurology and Neurophysiology, Medical Centre-University of Freiburg, Faculty of Medicine, University of Freiburg, 79106 Freiburg, Germany

Claus-Peter Schwartkop (CP)

Clinic for Neurology, Medical Centre Itzehoe, 25524 Itzehoe, Germany

Marco Berning (M)

Department of Medicine I, University Medical Center Dresden, Technische Universität (TU) Dresden, 01307 Dresden, Germany

Oliver Goetze (O)

Division of Hepatology, Department of Medicine II, University Hospital Wurzburg, 97080 Würzburg, Germany

Marcus Panning (M)

Institute of Virology, Medical Center - University of Freiburg, Faculty of Medicine, University of Freiburg, 79104 Freiburg, Germany

Miriam Fritz-Weltin (M)

Clinic of Neurology and Neurophysiology, Medical Centre-University of Freiburg, Faculty of Medicine, University of Freiburg, 79106 Freiburg, Germany

George Trendelenburg (G)

Clinic for Neurology, Medical Centre Itzehoe, 25524 Itzehoe, Germany
Department of Neurology, University Medical Centre Göttingen, 37075 Göttingen, Germany

Mathias Gelderblom (M)

Clinic for Neurology, University Medical Centre Hamburg-Eppendorf, 20251 Hamburg, Germany

Marc Lütgehetmann (M)

Institute of Medical Microbiology, Virology and Hygiene, University Medical Centre Hamburg-Eppendorf, 20251 Hamburg, Germany
German Center for Infection Research (DZIF), Hamburg-Lübeck-Borstel and Heidelberg Partner Sites, 20359 Hamburg, Germany

Fridrike Stute (F)

Clinic for Pediatrics, University Medical Centre Hamburg-Eppendorf, 20251 Hamburg, Germany

Thomas Horvatits (T)

Department of Medicine, University Medical Centre Hamburg-Eppendorf, 20251 Hamburg, Germany
German Center for Infection Research (DZIF), Hamburg-Lübeck-Borstel and Heidelberg Partner Sites, 20359 Hamburg, Germany

Meike Dirks (M)

Clinic for Neurology and Neurophysiology, Medical School Hannover, 30625 Hannover, Germany

Christoph Antoni (C)

Department of Medicine, University Medical Centre Mannheim, 68167 Mannheim, Germany

Patrick Behrendt (P)

Department of Medicine II, University Medical Center Mannheim, Medical Faculty Mannheim, Heidelberg University, 68167 Mannheim, Germany

Sven Pischke (S)

Department of Medicine, University Medical Centre Hamburg-Eppendorf, 20251 Hamburg, Germany
German Center for Infection Research (DZIF), Hamburg-Lübeck-Borstel and Heidelberg Partner Sites, 20359 Hamburg, Germany

Classifications MeSH