Extrarenal rhabdoid tumour of the vulva: diagnostic and management challenges.
cancer - see oncology
cancer intervention
Journal
BMJ case reports
ISSN: 1757-790X
Titre abrégé: BMJ Case Rep
Pays: England
ID NLM: 101526291
Informations de publication
Date de publication:
02 Jun 2021
02 Jun 2021
Historique:
entrez:
4
6
2021
pubmed:
5
6
2021
medline:
8
6
2021
Statut:
epublish
Résumé
Extrarenal rhabdoid tumour (ERT) of vulva is a rare gynaecological neoplasm with an aggressive course and no clear management guidelines. We present the case of a 25-year-old woman with a rapidly increasing mass in right vulva suggestive of sarcoma. Wide local excision was done. Histopathology examination revealed ERT of vulva. Six weeks later she manifested lung metastases. Despite adjuvant chemotherapy, the disease progressed and she died 8 months later. We review the literature and briefly discuss the epidemiology, treatment approaches, prognostic factors and expected outcomes of this rare disease.
Identifiants
pubmed: 34083195
pii: 14/6/e242271
doi: 10.1136/bcr-2021-242271
pmc: PMC8174509
pii:
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Informations de copyright
© BMJ Publishing Group Limited 2021. No commercial re-use. See rights and permissions. Published by BMJ.
Déclaration de conflit d'intérêts
Competing interests: None declared.
Références
Case Rep Med. 2011;2011:162709
pubmed: 21977040
Tumori. 1996 Jan-Feb;82(1):93-5
pubmed: 8623515
Am J Surg Pathol. 1997 Feb;21(2):130-46
pubmed: 9042279
Histopathology. 1990 Dec;17(6):576-8
pubmed: 2076893
Taiwan J Obstet Gynecol. 2016 Feb;55(1):128-30
pubmed: 26927265
Gynecol Oncol. 2001 Jan;80(1):99-103
pubmed: 11136579
Eur J Gynaecol Oncol. 1999;20(4):258-61
pubmed: 10475117
Curr Surg. 2002 Nov-Dec;59(6):570-1
pubmed: 16093195
Am J Surg Pathol. 1989 Oct;13(10):848-58
pubmed: 2476944
Pathol Int. 1998 Nov;48(11):887-91
pubmed: 9832058
J Cancer Res Ther. 2010 Jan-Mar;6(1):82-5
pubmed: 20479553
Int J Gynaecol Obstet. 2009 Jul;106(1):70-1
pubmed: 19342050
Cancer. 1978 May;41(5):1937-48
pubmed: 206343
Gynecol Oncol. 2007 Oct;107(1):130-5
pubmed: 17692365