The Unforeseen Diagnosis: Hyperparathyroidism-Jaw Tumour Syndrome Case Report and Review of the Literature.


Journal

Case reports in endocrinology
ISSN: 2090-6501
Titre abrégé: Case Rep Endocrinol
Pays: United States
ID NLM: 101576457

Informations de publication

Date de publication:
2021
Historique:
received: 01 02 2021
revised: 20 04 2021
accepted: 30 04 2021
entrez: 9 6 2021
pubmed: 10 6 2021
medline: 10 6 2021
Statut: epublish

Résumé

Hypercalcaemia and its systemic sequelae are a relatively common finding amongst patients in the field of endocrinology. Primary hyperparathyroidism, a frequent cause of hypercalcaemia, is often seen among middle-aged female patients, typically resulting from an underlying single-gland adenoma. Although patients may present with symptoms (nephrolithiasis, musculoskeletal discomfort, dehydration, or mood disturbance, to name a few), hypercalcaemia is rather frequently identified incidentally. In younger patients, a familial form of primary hyperparathyroidism must be considered, with a positive diagnosis mandating familial screening. Hyperparathyroidism-jaw tumour syndrome is one such autosomal dominant familial disorder, characterised by a mutation in the cell division cycle 73 (CDC73; also known as HRPT-2) tumour suppressor gene. This disorder is characterised by multiple pleiotropic phenomena, including recurrent primary hyperparathyroidism (and the effects of hypercalcaemia), neoplasms (such as uterine, renal, mandibular, and maxillary), and infertility. A patient not conforming to the classic candidacy for primary hyperparathyroidism requires consideration for a familial cause.

Identifiants

pubmed: 34104498
doi: 10.1155/2021/5551203
pmc: PMC8159647
doi:

Types de publication

Case Reports

Langues

eng

Pagination

5551203

Informations de copyright

Copyright © 2021 Maxim Barnett et al.

Déclaration de conflit d'intérêts

The authors declare that they have no conflicts of interest.

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Auteurs

Maxim Barnett (M)

University of Buckingham Medical School, Hunter St, Buckingham MK18 1EG, UK.

Farhan Ahmed (F)

Milton Keynes University Hospital, Standing Way, Eaglestone, Milton Keynes MK6 5LD, UK.

Radu Mihai (R)

Oxford Radcliffe Hospitals NHS Foundation Trust, Old Road, Headington, Oxford OX3 7LH, UK.

Asha Rattan (A)

University of Buckingham Medical School, Hunter St, Buckingham MK18 1EG, UK.

Malik Asif Humayun (MA)

Milton Keynes University Hospital, Standing Way, Eaglestone, Milton Keynes MK6 5LD, UK.

Classifications MeSH