Obeticholic Acid and Fibrates in Primary Biliary Cholangitis: Comparative Effects in a Multicentric Observational Study.


Journal

The American journal of gastroenterology
ISSN: 1572-0241
Titre abrégé: Am J Gastroenterol
Pays: United States
ID NLM: 0421030

Informations de publication

Date de publication:
01 11 2021
Historique:
received: 30 12 2020
accepted: 06 05 2021
pubmed: 24 6 2021
medline: 25 11 2021
entrez: 23 6 2021
Statut: ppublish

Résumé

Obeticholic acid (OCA) and fibrates therapy results in biochemical improvement in placebo-controlled trials in patients with primary biliary cholangitis and insufficient response to ursodeoxycholic acid. There is scarce information outside of clinical trials. Therefore, we have assessed the effectiveness and adverse events of these treatments. Data from patients included in the ColHai registry treated with OCA, fibrates, or both were recorded during a year, as well as adverse events and treatment discontinuation. Eighty-six patients were treated with OCA, 250 with fibrates (81% bezafibrate; 19% fenofibrate), and 15 with OCA plus fibrates. OCA group had baseline significantly higher alkaline phosphatase (ALP) (P = 0.01) and lower platelets (P = 0.03) than fibrates. Both treatments significantly decreased ALP, gamma-glutamyl transferase (GGT), and transaminases and improved Globe score. Albumin and immunoglobulin type M improved in the fibrates group. ALP decrease was higher under fibrates, whereas alanine aminotransferase decline was higher under OCA. Although baseline transaminases and GGT were higher in patients with OCA plus fibrates, significant ALP, GGT, alanine aminotransferase, and Globe score improvement were observed during triple therapy. Adverse events were reported in 14.7% of patients (21.3% OCA; 17.6% fenofibrate; 10.7% bezafibrate), mainly pruritus (10.1% with OCA). Discontinuation was more frequent in fenofibrate treatment mainly because of intolerance or adverse events. Second-line therapy with OCA or fibrates improves hepatic biochemistry and the GLOBE score in primary biliary cholangitis patients with suboptimal response to ursodeoxycholic acid. Simultaneous treatment with OCA and fibrates improved ALP as well.

Identifiants

pubmed: 34158466
doi: 10.14309/ajg.0000000000001343
pii: 00000434-202111000-00020
doi:

Substances chimiques

obeticholic acid 0462Z4S4OZ
Chenodeoxycholic Acid 0GEI24LG0J
Fenofibrate U202363UOS
Bezafibrate Y9449Q51XH

Types de publication

Comparative Study Journal Article Multicenter Study Observational Study Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

2250-2257

Informations de copyright

Copyright © 2021 by The American College of Gastroenterology.

Références

Parés A, Caballería L, Rodés J. Excellent long-term survival in patients with primary biliary cirrhosis and biochemical response to ursodeoxycholic acid. Gastroenterology 2006;130(3):715–20.
Kuiper EM, Hansen BE, de Vries RA, et al. Improved prognosis of patients with primary biliary cirrhosis that have a biochemical response to ursodeoxycholic acid. Gastroenterology 2009;136(4):1281–7.
Corpechot C, Abenavoli L, Rabahi N, et al. Biochemical response to ursodeoxycholic acid and long-term prognosis in primary biliary cirrhosis Hepatology 2008;48(3):871–7.
Corpechot C, Chazouillères O, Poupon R. Early primary biliary cirrhosis: Biochemical response to treatment and prediction of long-term outcome. J Hepatol 2011;55(6):1361–7.
Kumagi T, Guindi M, Fischer SE, et al. Baseline ductopenia and treatment response predict long-term histological progression in primary biliary cirrhosis. Am J Gastroenterol 2010;105(10):2186–94.
Hirschfield GM, Mason A, Luketic V, et al. Efficacy of obeticholic acid in patients with primary biliary cirrhosis and inadequate response to ursodeoxycholic acid. Gastroenterology 2015;148(4):751–61.
Kowdley KV, Luketic V, Chapman R, et al. A randomized trial of obeticholic acid monotherapy in patients with primary biliary cholangitis. Hepatology 2018;67(5):1890–902.
Nevens F, Andreone P, Mazzella G, et al. A placebo-controlled trial of obeticholic acid in primary biliary cholangitis. N Engl J Med 2016;375(7):631–43.
Honda A, Ikegami T, Nakamuta M, et al. Anticholestatic effects of bezafibrate in patients with primary biliary cirrhosis treated with ursodeoxycholic acid. Hepatology 2013;57(5):1931–41.
Hosonuma K, Sato K, Yamazaki Y, et al. A prospective randomized controlled study of long-term combination therapy using ursodeoxycholic acid and bezafibrate in patients with primary biliary cirrhosis and dyslipidemia. Am J Gastroenterol 2015;110(3):423–31.
Reig A, Sesé P, Parés A. Effects of bezafibrate on outcome and pruritus in primary biliary cholangitis with suboptimal ursodeoxycholic acid response. Am J Gastroenterol 2018;113(1):49–55.
Corpechot C, Chazouillères O, Rousseau A, et al. A placebo-controlled trial of bezafibrate in primary biliary cholangitis. N Engl J Med 2018;378(23):2171–81.
Honda A, Tanaka A, Kaneko T, et al. Bezafibrate improves GLOBE and UK-PBC scores and long-term outcomes in patients with primary biliary cholangitis. Hepatology 2019;70(6):2035–46.
Hegade VS, Khanna A, Walker LJ, et al. Long-term fenofibrate treatment in primary biliary cholangitis improves biochemistry but not the UK-PBC risk score. Dig Dis Sci 2016;61(10):3037–44.
Pellicciari R, Fiorucci S, Camaioni E, et al. 6alpha-ethyl-chenodeoxycholic acid (6-ECDCA), a potent and selective FXR agonist endowed with anticholestatic activity. J Med Chem 2002;45(17):3569–72.
Boyer JL, Trauner M, Mennone A, et al. Upregulation of a basolateral FXR-dependent bile acid efflux transporter OSTalpha-OSTbeta in cholestasis in humans and rodents. Am J Physiol Gastrointest Liver Physiol 2006;290(6):G1124–30.
Trauner M, Nevens F, Shiffman ML, et al. Long-term efficacy and safety of obeticholic acid for patients with primary biliary cholangitis: 3-year results of an international open-label extension study. Lancet Gastroenterol Hepatol 2019;4(6):445–53.
Bowlus CL, Pockros PJ, Kremer AE, et al. Long-term obeticholic acid therapy improves histological endpoints in patients with primary biliary cholangitis. Clin Gastroenterol Hepatol 2020;18(5):1170–8.
Lammers WJ, Hirschfield GM, Corpechot C, et al. Development and validation of a scoring system to predict outcomes of patients with primary biliary cirrhosis receiving ursodeoxycholic acid Ther Gastroenterol 2015;149(7):1804–1812.
Carbone M, Sharp SJ, Flack S, et al. The UK-PBC risk scores: Derivation and validation of a scoring system for long-term prediction of end-stage liver disease in primary biliary cholangitis Hepatology 2016;63(3):930–50.
Roberts SB, Ismail M, Kanagalingam G, et al. Real-world effectiveness of obeticholic acid in patients with primary biliary cholangitis. Hepatol Commun 2020;4(6):1332–45.

Auteurs

Anna Reig (A)

Liver Unit, Hospital Clínic, Universitat de Barcelona, IDIBAPS, Barcelona, Spain.
CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.

Carmen Álvarez-Navascués (C)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Central de Asturias, Oviedo, Spain.

Mercedes Vergara (M)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Unidad de Hepatología, Servicio de Aparato Digestivo, Parc Taulí Hospital Universitari, Institut d'Investigació i Innovació Parc Taulí I3PT, Universitat Autonoma de Barcelona, Sabadell, Instituto Carlos III, Bellaterra, Spain.

Elena Gómez-Domínguez (E)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital 12 de Octubre, Madrid, Spain.

Adolfo Gallego-Moya (A)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Santa Creu i Sant Pau, Barcelona, Spain.

Indhira M Pérez-Medrano (IM)

Unidad de Hepatología, Servicio de Aparato Digestivo, Complejo Hospitalario Universitario de Pontevedra & IIS Galicia Sur, Pontevedra, Spain.

Emilio Fábrega (E)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Marqués de Valdecilla, Santander, Spain.

Manuel Hernández-Guerra (M)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario de Canarias, Santa Cruz de Tenerife, Spain.

Marina Berenguer (M)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario e IIS la Fe, Valencia, Spain.
Universidad de Valencia, Valencia, Spain.

Pamela Estevez (P)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Álvaro Cunqueiro Pontevedra, Vigo, Spain.

Ana Arencibia (A)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Nuestra Señora de la Candelaria, Santa Cruz de Tenerife, Spain.

Rosa M Morillas (RM)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Hepatology Department, Hospital Germans Trias i Pujol, Badalona, Research institute, IGPT, Badalona, Universitat Autonoma de Barcelona, Barcelona, Spain.

Diana Horta (D)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Mútua de Terrassa, Terrassa, Spain.

Agustín Albillos (A)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Servicio de Gastroenterología, Hospital Universitario Ramón y Cajal, Universidad de Alcalá, IRYCIS, Madrid, Spain.

Marta Casado (M)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Torrecárdenas, Almería, Spain.

Gema De la Cruz (G)

Unidad de Hepatología, Servicio de Aparato Digestivo, Complejo Hospitalario Universitario de Toledo, Toledo, Spain.

Eva Fernandez-Bonilla (E)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Miguel Servet, Zaragoza, Spain.

Esther Molina (E)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Clínico De Santiago de Compostela, Santiago de Compostela, Spain.

Lander Hijona (L)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Osi Arraba Txagorritxu, Vitoria-Gasteiz, Spain.

Moises Diago (M)

Unidad de Hepatología, Servicio de Aparato Digestivo, Consorcio Hospital General de Valencia, Valencia, Spain.

Conrado M Fernández-Rodriguez (CM)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Fundación Universidad Rey Juan Carlos, Madrid, Alcorcón, Alcorcón, Spain.

Jesús M González-Santiago (JM)

Unidad de Hepatología, Servicio de Aparato Digestivo, Complejo Asistencial Universitario de Salamanca, ISBAL, Salamanca, Spain.

Margarita Sala (M)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Josep Trueta, Girona, Spain.

Judith Gómez-Camarero (J)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario de Burgos, Burgos, Spain.

Manuel Romero-Gomez (M)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Virgen del Rocío, Sevilla, Spain.

Francisco Suárez (F)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario A Coruña, A Coruña, Spain.

Victor Vargas (V)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Servicio Medicina Interna - Hepatología, Hospital Vall d'Hebron, Universidad Autónoma de Barcelona, Barcelona , Spain.

Carlos Ferre-Aracil (C)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitario Puerta de Hierro Majadahonda, Majadahonda, Spain.

Raúl J Andrade (RJ)

CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.
Unidad de Gestión Clínica de Aparato Digestivo, Instituto de Investigación Biomédica de Málaga-IBIMA. Hospital Universitario Virgen de la Victoria, Universidad de Málaga, a Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas, Málaga, Spain.

Nadia Chahri (N)

Unidad de Hepatología, Servicio de Aparato Digestivo, Hospital Universitari Sagrat Cor, Barcelona, Spain.

Albert Parés (A)

Liver Unit, Hospital Clínic, Universitat de Barcelona, IDIBAPS, Barcelona, Spain.
CIBEREHD Instituto de Salud Carlos III, Madrid, Spain.

Articles similaires

[Redispensing of expensive oral anticancer medicines: a practical application].

Lisanne N van Merendonk, Kübra Akgöl, Bastiaan Nuijen
1.00
Humans Antineoplastic Agents Administration, Oral Drug Costs Counterfeit Drugs

Smoking Cessation and Incident Cardiovascular Disease.

Jun Hwan Cho, Seung Yong Shin, Hoseob Kim et al.
1.00
Humans Male Smoking Cessation Cardiovascular Diseases Female
Humans United States Aged Cross-Sectional Studies Medicare Part C
1.00
Humans Yoga Low Back Pain Female Male

Classifications MeSH