Generalized Arterial Calcification of Infancy Type 1 (GACI1): Identification of a Novel Pathogenic Variant (c.1715T>C (p.Leu572Ser)).

ENPP1 gene GACI arterial calcifications autopsy mutations pathogenic variant

Journal

Diagnostics (Basel, Switzerland)
ISSN: 2075-4418
Titre abrégé: Diagnostics (Basel)
Pays: Switzerland
ID NLM: 101658402

Informations de publication

Date de publication:
04 Jun 2021
Historique:
received: 24 02 2021
revised: 29 05 2021
accepted: 30 05 2021
entrez: 2 7 2021
pubmed: 3 7 2021
medline: 3 7 2021
Statut: epublish

Résumé

Generalized Arterial Calcification of Infancy (GACI) is a rare disease inherited in a recessive manner, with severe and diffuse early onset of calcifications along the internal elastic lamina in large and medium size arteries. The diagnosis results are from clinical manifestations, imaging, histopathologic exams, and genetic tests. GACI is predominantly caused by biallelic pathogenic variant in the

Identifiants

pubmed: 34199854
pii: diagnostics11061034
doi: 10.3390/diagnostics11061034
pmc: PMC8229691
pii:
doi:

Types de publication

Journal Article

Langues

eng

Références

Circ Cardiovasc Genet. 2008 Dec;1(2):133-40
pubmed: 20016754
Am J Hum Genet. 2012 Jan 13;90(1):25-39
pubmed: 22209248
Curr Osteoporos Rep. 2017 Aug;15(4):255-270
pubmed: 28585220
J Dent Res. 2018 Apr;97(4):432-441
pubmed: 29244957
Am J Med Genet A. 2019 Oct;179(10):2112-2118
pubmed: 31444901
Genet Med. 2015 May;17(5):405-24
pubmed: 25741868
J Bone Miner Res. 2020 Mar;35(3):528-539
pubmed: 31805212
Hum Mutat. 2016 Nov;37(11):1190-1201
pubmed: 27467858
Nat Genet. 2003 Aug;34(4):379-81
pubmed: 12881724
BMC Pediatr. 2018 Jul 5;18(1):217
pubmed: 29976176

Auteurs

Gaetano Pietro Bulfamante (GP)

Human Pathology and Medical Genetic Unit, Department of Health Sciences, San Paolo Hospital, University of Milan, 20142 Milan, Italy.

Laura Carpenito (L)

School of Pathology, University of Milan, 20122 Milan, Italy.

Emma Bragantini (E)

Department of Pathology, Santa Chiara Hospital, 38122 Trento, Italy.

Silvia Graziani (S)

NICU, Santa Chiara Hospital, 38122 Trento, Italy.

Maria Bellizzi (M)

Department of Pediatrics, Santa Chiara Hospital, 38122 Trento, Italy.

Christoph Peter Bagowski (CP)

Prenatal Medicine Münich, Department of Molecular Genetics, University Hospital, Aiblingerstr. 8, 80639 Münich, Germany.

Moneef Shoukier (M)

Prenatal Medicine Münich, Department of Molecular Genetics, University Hospital, Aiblingerstr. 8, 80639 Münich, Germany.

Francesca Rivieri (F)

Medical Genetic Service, Santa Chiara Hospital, 38122 Trento, Italy.

Massimo Soffiati (M)

Department of Pediatrics, Santa Chiara Hospital, 38122 Trento, Italy.

Mattia Barbareschi (M)

Department of Pathology, Santa Chiara Hospital, 38122 Trento, Italy.

Classifications MeSH