Renal neoplasms in tuberous sclerosis mice are neurocristopathies.
cancer;
molecular physiology
stem cells research
Journal
iScience
ISSN: 2589-0042
Titre abrégé: iScience
Pays: United States
ID NLM: 101724038
Informations de publication
Date de publication:
23 Jul 2021
23 Jul 2021
Historique:
received:
15
12
2020
revised:
20
04
2021
accepted:
31
05
2021
entrez:
5
7
2021
pubmed:
6
7
2021
medline:
6
7
2021
Statut:
epublish
Résumé
Tuberous sclerosis (TS) is a rare disorder exhibiting multi-systemic benign neoplasms. We hypothesized the origin of TS neoplastic cells derived from the neural crest given the heterogeneous ecto-mesenchymal phenotype of the most common TS neoplasms. To test this hypothesis, we employed Cre-loxP lineage tracing of myelin protein zero (Mpz)-expressing neural crest cells (NCCs) in spontaneously developing renal tumors of
Identifiants
pubmed: 34222844
doi: 10.1016/j.isci.2021.102684
pii: S2589-0042(21)00652-0
pmc: PMC8243016
doi:
Types de publication
Journal Article
Langues
eng
Pagination
102684Informations de copyright
© 2021 The Authors.
Déclaration de conflit d'intérêts
The authors declare no competing interests.
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