The Role of Imaging in Diagnosing Transthyretin Cardiac Amyloidosis.
99mtc-pyp scintigraphy
cardiac amyloidosis
cardiovascular magnetic resonance imaging
hereditary attr amyloidosis
left ventricular hypertrophy
transthyretin
Journal
Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737
Informations de publication
Date de publication:
Jun 2021
Jun 2021
Historique:
accepted:
05
06
2021
entrez:
15
7
2021
pubmed:
16
7
2021
medline:
16
7
2021
Statut:
epublish
Résumé
Cardiac amyloidosis is a rare underdiagnosed condition with increasing morbidity and mortality. Its diagnosis is challenging and requires high clinical suspicion. Several diagnostic tools aid in the diagnosis of cardiac amyloidosis such as electrocardiogram, echocardiography, and, most importantly, cardiac MRI. A wide range of clinical symptoms is associated with cardiac amyloidosis, with shortness of breath and peripheral edema being the most common presenting complaints. Here, we report a case of transthyretin cardiac amyloidosis and discuss the importance of imaging in establishing the diagnosis.
Identifiants
pubmed: 34262806
doi: 10.7759/cureus.15468
pmc: PMC8260218
doi:
Types de publication
Case Reports
Langues
eng
Pagination
e15468Informations de copyright
Copyright © 2021, Chaaban et al.
Déclaration de conflit d'intérêts
The authors have declared that no competing interests exist.
Références
Circulation. 2016 Jun 14;133(24):2404-12
pubmed: 27143678
JACC Cardiovasc Imaging. 2014 Feb;7(2):157-65
pubmed: 24412190
J Am Coll Cardiol. 2008 Mar 11;51(10):1022-30
pubmed: 18325442
Amyloid. 2016 Dec;23(4):209-213
pubmed: 27884064
Circulation. 2012 Sep 4;126(10):1286-300
pubmed: 22949539
Fac Rev. 2021 Mar 24;10:31
pubmed: 33817700
Curr Opin Pharmacol. 2006 Apr;6(2):214-20
pubmed: 16483845
An Sist Sanit Navar. 2018 Aug 29;41(2):263-267
pubmed: 29943762
JACC Cardiovasc Imaging. 2011 Nov;4(11):1206-16
pubmed: 22093272
Curr Cardiol Rep. 2019 Aug 2;21(9):108
pubmed: 31375984
Blood. 2013 Apr 25;121(17):3420-7
pubmed: 23479568
Int J Cardiol. 2016 Jul 1;214:477-81
pubmed: 27093686
Am J Cardiol. 2014 Oct 1;114(7):1089-93
pubmed: 25212550
J Am Coll Cardiol. 2005 Sep 20;46(6):1076-84
pubmed: 16168294