Cor triatriatum with supramitral ring: "cor tetratriatum", associated with Raghib syndrome with Eisenmenger syndrome: multimodality imaging approach in this exceedingly rare case report.
Case report
Congenital heart disease
Cor tetratriatum
Cor triatriatum
Cyanosis
Eisenmenger syndrome
Persistent left superior vena cava
Raghib syndrome
Supramitral ring
Unroofed coronary sinus
Journal
The Egyptian heart journal : (EHJ) : official bulletin of the Egyptian Society of Cardiology
ISSN: 2090-911X
Titre abrégé: Egypt Heart J
Pays: Germany
ID NLM: 9106952
Informations de publication
Date de publication:
17 Jul 2021
17 Jul 2021
Historique:
received:
21
01
2021
accepted:
10
06
2021
entrez:
17
7
2021
pubmed:
18
7
2021
medline:
18
7
2021
Statut:
epublish
Résumé
Cor triatriatum and supramitral ring are congenital anomalies which result in formation of three chambers of atria. To the best of our knowledge, simultaneous presence of both entities in the same patient resulting in the formation of four chambers of atria has not been described in the literature. Here, we report a case of simultaneous presence of cor triatriatum and supramitral ring associated with Raghib syndrome and Eisenmenger syndrome. We report the case of a middle-aged gentleman, who presented to us with features of atrial septal defect with Eisenmenger syndrome. Multimodality imaging confirmed the simultaneous presence of supramital ring and cor triatriatum resulting in "cor tetratriatum" along with Raghib syndrome. Presence of Eisenmenger syndrome compelled us to offer medical therapy for the patient. This is the first case report describing the simultaneous presence of supramitral ring and cor triatriatum resulting in a new entity-"cor tetratriatum".
Sections du résumé
BACKGROUND
BACKGROUND
Cor triatriatum and supramitral ring are congenital anomalies which result in formation of three chambers of atria. To the best of our knowledge, simultaneous presence of both entities in the same patient resulting in the formation of four chambers of atria has not been described in the literature. Here, we report a case of simultaneous presence of cor triatriatum and supramitral ring associated with Raghib syndrome and Eisenmenger syndrome.
CASE PRESENTATION
METHODS
We report the case of a middle-aged gentleman, who presented to us with features of atrial septal defect with Eisenmenger syndrome. Multimodality imaging confirmed the simultaneous presence of supramital ring and cor triatriatum resulting in "cor tetratriatum" along with Raghib syndrome. Presence of Eisenmenger syndrome compelled us to offer medical therapy for the patient.
CONCLUSION
CONCLUSIONS
This is the first case report describing the simultaneous presence of supramitral ring and cor triatriatum resulting in a new entity-"cor tetratriatum".
Identifiants
pubmed: 34273027
doi: 10.1186/s43044-021-00183-4
pii: 10.1186/s43044-021-00183-4
pmc: PMC8286211
doi:
Types de publication
Journal Article
Langues
eng
Pagination
66Informations de copyright
© 2021. The Author(s).
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