IgG4-related sclerosing cholangitis: not always an obvious entity.

IgG4-related sclerosing cholangitis cholangiocarcinoma

Journal

Annals of gastroenterology
ISSN: 1108-7471
Titre abrégé: Ann Gastroenterol
Pays: Greece
ID NLM: 101121847

Informations de publication

Date de publication:
Historique:
received: 23 11 2020
accepted: 11 12 2020
entrez: 19 7 2021
pubmed: 20 7 2021
medline: 20 7 2021
Statut: ppublish

Résumé

Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a distinct type of cholangitis, currently recognized as a biliary manifestation of IgG4-related disease. We present a case of type 3 IgG4-SC in a patient with normal IgG4 serum levels, surgically treated for suspicion of cholangiocarcinoma. This case highlights that differentiating between isolated IgG4-SC and cholangiocarcinoma can present a challenging diagnostic dilemma.

Identifiants

pubmed: 34276201
doi: 10.20524/aog.2021.0610
pii: AnnGastroenterol-34-594
pmc: PMC8276355
doi:

Types de publication

Case Reports

Langues

eng

Pagination

594-596

Informations de copyright

Copyright: © Hellenic Society of Gastroenterology.

Déclaration de conflit d'intérêts

Conflict of Interest: None

Références

Hum Pathol. 2014 Aug;45(8):1722-9
pubmed: 24890945
J Gastroenterol Hepatol. 2013 Jul;28(7):1247-51
pubmed: 23621484
Mod Pathol. 2012 Sep;25(9):1181-92
pubmed: 22596100
J Gastroenterol. 2012 Jan;47(1):79-87
pubmed: 21947649
Gastroenterology. 2008 Mar;134(3):706-15
pubmed: 18222442
Hepatology. 2011 Sep 2;54(3):940-8
pubmed: 21674559
Lancet. 2015 Apr 11;385(9976):1460-71
pubmed: 25481618
Gastrointest Endosc. 2016 Oct;84(4):649-55
pubmed: 26995690
J Gastroenterol. 2011 May;46(5):696-704
pubmed: 21188426
J Hepatobiliary Pancreat Sci. 2012 Sep;19(5):536-42
pubmed: 22717980

Auteurs

Magdalini Velegraki (M)

Department of Gastroenterology, Venizeleion General Hospital, Heraklion (Magdalini Velegraki, Emmanouil Vardas, Maria Fragaki, Pinelopi Nikolaou, Afroditi Mpitouli, Gregorios A. Paspatis).

Emmanouil Vardas (E)

Department of Gastroenterology, Venizeleion General Hospital, Heraklion (Magdalini Velegraki, Emmanouil Vardas, Maria Fragaki, Pinelopi Nikolaou, Afroditi Mpitouli, Gregorios A. Paspatis).

Christos Dervenis (C)

Hepatobiliary and Pancreatic Surgery Clinic, Metropolitan Hospital, Athens (Christos Dervenis).

Maria Fragaki (M)

Department of Gastroenterology, Venizeleion General Hospital, Heraklion (Magdalini Velegraki, Emmanouil Vardas, Maria Fragaki, Pinelopi Nikolaou, Afroditi Mpitouli, Gregorios A. Paspatis).

Pinelopi Nikolaou (P)

Department of Gastroenterology, Venizeleion General Hospital, Heraklion (Magdalini Velegraki, Emmanouil Vardas, Maria Fragaki, Pinelopi Nikolaou, Afroditi Mpitouli, Gregorios A. Paspatis).

Afroditi Mpitouli (A)

Department of Gastroenterology, Venizeleion General Hospital, Heraklion (Magdalini Velegraki, Emmanouil Vardas, Maria Fragaki, Pinelopi Nikolaou, Afroditi Mpitouli, Gregorios A. Paspatis).

George Kazamias (G)

Department of Histopathology, Venizeleion General Hospital, Heraklion (George Kazamias, Elpida Giannikaki).

Athanasia Sepsa (A)

Department of Histopathology, Metropolitan Hospital, Athens (Athanasia Sepsa), Greece.

Elpida Giannikaki (E)

Department of Histopathology, Venizeleion General Hospital, Heraklion (George Kazamias, Elpida Giannikaki).

Gregorios A Paspatis (GA)

Department of Gastroenterology, Venizeleion General Hospital, Heraklion (Magdalini Velegraki, Emmanouil Vardas, Maria Fragaki, Pinelopi Nikolaou, Afroditi Mpitouli, Gregorios A. Paspatis).

Classifications MeSH