Favorable outcomes of interferon-α and ribavirin treatment for a male with subacute sclerosing panencephalitis.


Journal

Journal of neuroimmunology
ISSN: 1872-8421
Titre abrégé: J Neuroimmunol
Pays: Netherlands
ID NLM: 8109498

Informations de publication

Date de publication:
15 09 2021
Historique:
received: 15 03 2021
revised: 21 06 2021
accepted: 05 07 2021
pubmed: 26 7 2021
medline: 24 12 2021
entrez: 25 7 2021
Statut: ppublish

Résumé

Subacute sclerosing panencephalitis (SSPE) is a slow virus infection associated with mutant measles virus (MeV). The long-term outcome of antiviral treatments remains to be determined. We herein present a Japanese boy who was diagnosed with SSPE at 10 years of age. Intraventricular infusions of interferon-α effectively prevented the progress of symptoms during 14 years of follow-up period. Flow-cytometric analysis demonstrated higher proportion of T helper 17 cells (Th17, 18.2%) than healthy controls (4.8-14.5%) despite the normal subpopulation of peripheral lymphocytes. These data suggest that a group of patients with SSPE may show favorable responses to intraventricular infusions of interferon-α.

Identifiants

pubmed: 34304142
pii: S0165-5728(21)00183-1
doi: 10.1016/j.jneuroim.2021.577656
pii:
doi:

Substances chimiques

Antiviral Agents 0
Interferon-alpha 0
Ribavirin 49717AWG6K

Types de publication

Case Reports Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

577656

Informations de copyright

Copyright © 2021 Elsevier B.V. All rights reserved.

Auteurs

Yuri Sonoda (Y)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan; Research Center for Environment and Developmental Medical Sciences, Kyushu University, Fukuoka, Japan.

Motoshi Sonoda (M)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.

Kousuke Yonemoto (K)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.

Masafumi Sanefuji (M)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan; Research Center for Environment and Developmental Medical Sciences, Kyushu University, Fukuoka, Japan.

Ryoji Taira (R)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.

Yoshitomo Motomura (Y)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.

Masataka Ishimura (M)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.

Hiroyuki Torisu (H)

Section of Pediatrics, Department of Medicine, Fukuoka Dental College, Fukuoka, Japan.

Ryutaro Kira (R)

Department of Pediatric Neurology, Fukuoka Children's Hospital, Fukuoka, Japan.

Koichi Kusuhara (K)

Department of Pediatrics, University of Occupational and Environmental Health, Kitakyushu, Japan.

Yasunari Sakai (Y)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan. Electronic address: ysakai22q13@gmail.com.

Shouichi Ohga (S)

Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.

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Classifications MeSH