Childhood pemphigus vulgaris is a challenging diagnosis.
Child
Fluorescent Antibody Technique, Direct
Pemphigus
Journal
Autopsy & case reports
ISSN: 2236-1960
Titre abrégé: Autops Case Rep
Pays: Brazil
ID NLM: 101640070
Informations de publication
Date de publication:
2021
2021
Historique:
received:
04
11
2020
accepted:
01
02
2021
entrez:
26
7
2021
pubmed:
27
7
2021
medline:
27
7
2021
Statut:
epublish
Résumé
Pemphigus Vulgaris (PV) is an uncommon autoimmune and blistering mucocutaneous disease. Childhood Pemphigus Vulgaris (CPV) is a pediatric variant of PV, which affects children below 12 years, being very rare among children under 10 years of age. CPV has similar clinical, histological, and immunological features as seen in PV in adults. The mucocutaneous clinical presentation is the most common in both age groups. Vesicles and erosions arising from the disease usually cause pain. A few CPV cases have been reported in the literature. This study reports a case of an 8-year-old male patient with oral lesions since the age of 3 years, and the diagnosis of pemphigus was achieved only 2 years after the appearance of the initial lesions. CPV remains a rare disease, making the diagnosis of this clinical case a challenge due to its age of onset and clinical features presented by the patient. Therefore, dentists and physicians should know how to differentiate CPV from other bullous autoimmune diseases more common in childhood.
Identifiants
pubmed: 34307224
doi: 10.4322/acr.2021.267
pii: acrep088520
pmc: PMC8294838
doi:
Types de publication
Case Reports
Langues
eng
Pagination
e2021267Informations de copyright
Copyright © 2021 The Authors.
Déclaration de conflit d'intérêts
Conflict of interest: The authors have no conflict of interest to declare.
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