Fontan Liver Lesions: Not Always HCC.
AASLD, American Association for Study of Liver Disease
AFP, alpha-fetoprotein
ALT, lanine aminotransferase
AST, aspartate aminotransferase
AV, atrioventricular
CT, computed tomography
FALD, Fontan associated liver disease
FNH, focal nodular hyperplasia
GS, glutamine synthetase
HCC, hepatocellular carcinoma
INR, international normalized ratio
MRI, magnetic resonance imaging
US, ultrasound
awareness
congenital heart defect
cyanotic heart disease
imaging
treatment
Journal
JACC. Case reports
ISSN: 2666-0849
Titre abrégé: JACC Case Rep
Pays: Netherlands
ID NLM: 101757292
Informations de publication
Date de publication:
Aug 2019
Aug 2019
Historique:
received:
10
05
2019
accepted:
29
05
2019
entrez:
28
7
2021
pubmed:
21
8
2019
medline:
21
8
2019
Statut:
epublish
Résumé
A 24-year-old Fontan procedure patient underwent surveillance liver cardiac magnetic resonance imaging. Findings were suggestive of hepatocellular carcinoma (HCC). Currently, HCC is diagnosed based on imaging alone. Given her otherwise reassuring clinical profile, she underwent liver biopsy. Pathology demonstrated focal nodular hyperplasia. This raises concern for overdiagnosis of HCC in Fontan patients without tissue confirmation. (
Identifiants
pubmed: 34316779
doi: 10.1016/j.jaccas.2019.05.031
pii: S2666-0849(19)30118-4
pmc: PMC8301494
doi:
Types de publication
Case Reports
Langues
eng
Pagination
175-178Informations de copyright
© 2019 The Authors.
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