A Rare Case of Severe Nontropical Isolated Right Ventricular Endomyocardial Fibrosis.

CE, contrast-enhanced CMR, cardiac magnetic resonance ECMO, extracorporeal membrane oxygenation EMF, endomyocardial fibrosis LV, left ventricular RA, right atrial RV, right ventricular RVOT, right ventricular outflow tract TTE, Transthoracic echocardiogram TV, tricuspid valve contrast enhanced TTE endomyocardial fibrosis right ventricle

Journal

JACC. Case reports
ISSN: 2666-0849
Titre abrégé: JACC Case Rep
Pays: Netherlands
ID NLM: 101757292

Informations de publication

Date de publication:
Nov 2020
Historique:
received: 13 03 2020
revised: 15 09 2020
accepted: 22 09 2020
entrez: 28 7 2021
pubmed: 29 7 2021
medline: 29 7 2021
Statut: epublish

Résumé

We present a case of late presentation nontropical endomyocardial fibrosis isolated to the right ventricle and tricuspid valve (TV). In response to deteriorating hemodynamics, surgical debulking and TV removal were performed before initiation of centralized venoarterial extracorporeal membrane oxygenation support. Definitive endomyocardial resection with a TV prosthesis was then successfully completed. (

Identifiants

pubmed: 34317112
doi: 10.1016/j.jaccas.2020.09.042
pii: S2666-0849(20)31197-9
pmc: PMC8299774
doi:

Types de publication

Case Reports

Langues

eng

Pagination

2078-2084

Informations de copyright

Crown Copyright © 2020 Published by Elsevier on behalf of the American College of Cardiology Foundation.

Déclaration de conflit d'intérêts

Dr. Platts is acting as a medical liaison for Lantheus Medical Imaging. All other authors have reported that they have no relationships relevant to the contents of this paper to disclose.

Références

PLoS Negl Trop Dis. 2008 Feb 27;2(2):e97
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N Engl J Med. 2008 Jul 3;359(1):43-9
pubmed: 18596273
Circulation. 2016 Jun 14;133(24):2503-15
pubmed: 27297343
Eur J Cardiothorac Surg. 1999 Mar;15(3):309-12; discussion 312-3
pubmed: 10333028
Heart. 2016 Jan;102(2):100-6
pubmed: 26567231

Auteurs

Shaaheen Laher (S)

Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.

Yee Weng Wong (YW)

Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.
Cardio-Vascular Molecular & Therapeutics Translational Research Group, University of Queensland, Brisbane, Australia.

David Platts (D)

Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.
Cardiology Program, The Prince Charles Hospital School of Medicine, University of Queensland School of Medicine, Griffith University, Brisbane, Australia.

Anil Prabhu (A)

Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.

Bruce Thomson (B)

Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.

Christian Hamilton-Craig (C)

Cardiology Program, The Prince Charles Hospital School of Medicine, University of Queensland School of Medicine, Griffith University, Brisbane, Australia.

David Godbolt (D)

Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.

Elizabeth Cheesman (E)

Cardio-Vascular Molecular & Therapeutics Translational Research Group, University of Queensland, Brisbane, Australia.

Alexander Dashwood (A)

Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.
Cardio-Vascular Molecular & Therapeutics Translational Research Group, University of Queensland, Brisbane, Australia.

Classifications MeSH