Comprehensive Risk Management in Arrhythmogenic Cardiomyopathy Associated With Autosomal Dominant Carvajal Syndrome: Protecting Families.

AC, arrhythmogenic cardiomyopathy Carvajal syndrome ECG, electrocardiogram LV, left ventricular RV, right ventricular arrhythmic risk cascade screening desmoplakin genetic testing sudden cardiac death

Journal

JACC. Case reports
ISSN: 2666-0849
Titre abrégé: JACC Case Rep
Pays: Netherlands
ID NLM: 101757292

Informations de publication

Date de publication:
Jun 2020
Historique:
received: 31 01 2020
revised: 23 03 2020
accepted: 27 03 2020
entrez: 28 7 2021
pubmed: 29 7 2021
medline: 29 7 2021
Statut: epublish

Résumé

In a 37-year-old cardiac arrest survivor with autosomal dominant Carvajal syndrome and arrhythmogenic cardiomyopathy, a desmoplakin mutation was identified. Cascade screening identified 2 affected family members and 2 healthy children carrying the mutation. Strategies for primary and secondary risk prevention emphasize the role of genetic testing in rare cardiomyopathies. (

Identifiants

pubmed: 34317383
doi: 10.1016/j.jaccas.2020.03.033
pii: S2666-0849(20)30377-6
pmc: PMC8302052
doi:

Types de publication

Case Reports

Langues

eng

Pagination

925-929

Informations de copyright

© 2020 The Authors.

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Auteurs

Maria Grazia De Gregorio (MG)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.

Francesca Girolami (F)

Cardiology Unit, Meyer University Hospital, Florence, Italy.

Benedetta Tomberli (B)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.

Guendalina Rossi (G)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.

Alessia Tomberli (A)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.

Katia Baldini (K)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.

Iacopo Olivotto (I)

Cardiomyopathy Unit, Careggi University Hospital, Florence, Italy.

Classifications MeSH