Biallelic

COA7/RESA1 COX assembly factor biallelic variant mitochondrial disease nervous system disorder

Journal

Frontiers in genetics
ISSN: 1664-8021
Titre abrégé: Front Genet
Pays: Switzerland
ID NLM: 101560621

Informations de publication

Date de publication:
2021
Historique:
received: 24 03 2021
accepted: 15 06 2021
entrez: 29 7 2021
pubmed: 30 7 2021
medline: 30 7 2021
Statut: epublish

Résumé

The cytochrome c oxidase assembly factor 7 ( We performed trio-exome sequencing in the affected patient and both parents. To verify the pathogenicity of the detected variants in A Chinese girl was referred at 9 months of age with a history of developmental delay and regression since 3 months of age. In the following months, she lost previously acquired skills and developed progressive spasticity of the lower extremities. Trio-exome sequencing revealed compound heterzygous variants in Hitherto, characteristic features of

Identifiants

pubmed: 34322155
doi: 10.3389/fgene.2021.685035
pmc: PMC8312223
doi:

Types de publication

Journal Article

Langues

eng

Pagination

685035

Informations de copyright

Copyright © 2021 Ban, Liu, Shimura, Tong, Wang, Yang, Xu, Xiao, Murayama, Elstner, Prokisch and Fang.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Rui Ban (R)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.
Institute of Human Genetics, Helmholtz Zentrum München, Munich, Germany.

Zhimei Liu (Z)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.

Masaru Shimura (M)

Institute of Human Genetics, Helmholtz Zentrum München, Munich, Germany.
Department of Metabolism, Chiba Children's Hospital, Chiba, Japan.

Xiao Tong (X)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.

Junling Wang (J)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.

Lei Yang (L)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.

Manting Xu (M)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.

Jing Xiao (J)

Department of Neurology, Beijing New Century International Children's Hospital, Beijing China.

Kei Murayama (K)

Department of Metabolism, Chiba Children's Hospital, Chiba, Japan.

Matthias Elstner (M)

Department of Neurology, School of Medicine, Technical University of Munich, Munich, Germany.

Holger Prokisch (H)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.
Institute of Human Genetics, Helmholtz Zentrum München, Munich, Germany.
Institute of Human Genetics, Technische Universität München, Munich, Germany.

Fang Fang (F)

Department of Neurology, National Center for Children's Health, Beijing Children's Hospital, Capital Medical University, Beijing, China.

Classifications MeSH